Churg-Strauss Syndrome with a Clinical Condition Similar to IgG4-Related Kidney Disease: A Case Report

被引：27

作者：

Ayuzawa, Nobuhiro ^{[1
,4
]}

Ubara, Yoshifumi ^{[1
,5
]}

Keiichi, Sumida ^{[1
]}

Masayuki, Yamanouchi ^{[1
]}

Hasegawa, Eiko ^{[1
]}

Hiramatsu, Eriko ^{[1
]}

Hayami, Noriko ^{[1
]}

Suwabe, Tatsuya ^{[1
]}

Hoshino, Junichi ^{[1
]}

Sawa, Naoki ^{[1
]}

Kawabata, Masateru ^{[2
]}

Ohashi, Kenichi ^{[3
]}

Takaichi, Kennmei ^{[1
,5
]}

机构：

[1] Toranomon Gen Hosp, Nephrol Ctr, Tokyo, Japan

[2] Toranomon Gen Hosp, Dept Resp Med, Tokyo, Japan

[3] Toranomon Gen Hosp, Dept Pathol, Tokyo, Japan

[4] Univ Tokyo, Grad Sch Med, Dept Nephrol & Endocrinol, Tokyo 1138654, Japan

[5] Toranomon Gen Hosp, Okinaka Mem Inst Med Res, Tokyo, Japan

来源：

INTERNAL MEDICINE | 2012年 / 51卷 / 10期

关键词：

IgG4-related kidney disease; Churg-Strauss syndrome; ANCA negative; membranous nephropathy; tubulointerstitial nephritis; ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES; TERM-FOLLOW-UP; AUTOIMMUNE PANCREATITIS; RENAL INVOLVEMENT; IGG4; PROPOSAL; CRITERIA; ASTHMA;

D O I：

10.2169/internalmedicine.51.6074

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 68-year-old Japanese woman with asthma of recent onset and a long history of membranous glomerulonephropathy (MN) was admitted because of multifocal pulmonary infiltrates, marked eosinophilia, mild renal dysfunction, a rash on her feet, and right median nerve paralysis. Although MPO- and PR3-ANCA were negative, skin biopsy demonstrated leukocytoclastic vasculitis and Churg-Strauss Syndrome (CSS) was diagnosed. She also had salivary gland swelling and a high serum IgG4 level. Renal biopsy revealed MN with eosinophil-rich tubulointerstitial nephropathy. Her symptoms resolved after the start of corticosteroid therapy. The present case shows that ANCA-negative CSS can have a clinical condition similar to IgG4-related kidney disease.

引用

页码：1233 / 1238

页数：6

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