Massive epithelioid angiomyolipoma of the kidney in a young girl

被引:9
作者
Hung, MS
Chang, JHM
Chang, CP
Tai, HL
机构
[1] Changhua Christian Hosp, Dept Surg, Div Urol, Changhua, Taiwan
[2] Changhua Christian Hosp, Dept Pathol, Changhua, Taiwan
[3] Chung Shan Med Univ, Inst Med, Taichung, Taiwan
关键词
epithelioid angiomyolipoma; pediatric;
D O I
10.1111/j.1442-2042.2005.01194.x
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
We report the case of a huge right renal tumor in a 17-year-old girl. Absence of fat on preoperative magnetic resonance imaging suggested renal cell carcinoma, and surgery was performed. Pathologic evaluation with HMB-45 immunohistochemical staining conrmed the diagnosis of epithelioid angiomyolipoma. The tumor consisted predominantly of epithelioid cells, and it could easily be misidentied as a renal cell carcinoma due to the paucity of the fat component. Previous reports have suggested that epithelioid angiomyolipomas have the potential to be malignant, and thus regular postoperative surveillance is recommended. Our patient had no signs of recurrence at her most recent follow up, 12 months after surgery.
引用
收藏
页码:998 / 1000
页数:3
相关论文
共 11 条
[1]  
ASHFAQ R, 1993, CANCER, V71, P3091, DOI 10.1002/1097-0142(19930515)71:10<3091::AID-CNCR2820711032>3.0.CO
[2]  
2-5
[3]   Estrogen receptor is significantly associated with the epithelioid variants of renal angiomyolipoma: A clinicopathological and immunohistochemical study of 67 cases [J].
Cho, NH ;
Shim, HS ;
Choi, YD ;
Kim, DS .
PATHOLOGY INTERNATIONAL, 2004, 54 (07) :510-515
[4]   Malignant epithelioid angiomyolipoma ('Sarcoma ex angiomyolipoma') of the kidney - A case report and review of the literature [J].
Cibas, ES ;
Goss, GA ;
Kulke, MH ;
Demetri, GD ;
Fletcher, CDM .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 2001, 25 (01) :121-126
[5]   Epithelioid angiomyolipoma of the kidney - A report of five cases with a prominent and diagnostically confusing epithelioid smooth muscle component [J].
Eble, JN ;
Amin, MB ;
Young, RH .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1997, 21 (10) :1123-1130
[6]   Renal angiomyolipoma with epithelioid sarcomatous transformation and metastases - Demonstration of the same genetic defects in the primary and metastatic lesions [J].
Martignoni, G ;
Pea, M ;
Rigaud, G ;
Manfrin, E ;
Colato, C ;
Zamboni, G ;
Scarpa, A ;
Tardanico, R ;
Roncalli, M ;
Bonetti, F .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 2000, 24 (06) :889-894
[7]   Carcinomalike monotypic epithelioid angiomyolipoma in patients without evidence of tuberous sclerosis - A clinicopathologic and genetic study [J].
Martignoni, G ;
Pea, M ;
Bonetti, F ;
Zamboni, G ;
Carbonara, C ;
Longa, L ;
Zancanaro, C ;
Maran, M ;
Brisigotti, M ;
Mariuzzi, GM .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1998, 22 (06) :663-672
[8]   Contemporary diagnosis and management of renal angiomyolipoma [J].
Nelson, CP ;
Sanda, MG .
JOURNAL OF UROLOGY, 2002, 168 (04) :1315-1325
[9]   Recurrent renal epithelioid angiomyolipoma [J].
Ong, A ;
Pinto, P ;
Kim, F ;
Kavoussi, L .
UROLOGY, 2003, 61 (05) :1035
[10]   Apparent renal cell carcinomas in tuberous sclerosis are heterogeneous - The identification of malignant epithelioid angiomyolipoma [J].
Pea, M ;
Bonetti, F ;
Martignoni, G ;
Henske, EP ;
Manfrin, E ;
Colato, C ;
Bernstein, J .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1998, 22 (02) :180-187