central nervous system;
crystal-storing histiocytosis;
electron microscopy;
intracellular crystals;
lymphoplasmacytic neoplasm;
NERVOUS-SYSTEM;
PATIENT;
GAMMOPATHY;
DIAGNOSIS;
DISORDER;
WOMAN;
MASS;
D O I:
10.1111/neup.12486
中图分类号:
R74 [神经病学与精神病学];
学科分类号:
摘要:
Crystal-storing histiocytosis (CSH) is an uncommon histiocytic proliferation reported to involve diverse organs and tissues, but involvement of the central nervous system (CNS) is rare. In most cases CSH is identified in association with underlying lymphoproliferative, plasma cell diseases or rarely with various inflammatory or infectious conditions. CSH is characterized by the cytoplasmic accumulation of crystalline material in histiocytes, most commonly of kappa immunoglobulin light chain. We report a unique case of localized CSH involving the left cerebellum and caudal brain stem in a young man with a history of gout but without known lymphoproliferative or plasma cell disorders. Awareness of this entity is important diagnostically, but also to ensure appropriate management and follow-up, particularly in the absence of apparent underlying malignancy.
机构:
Azienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Rossi, Giulio
De Rosa, Nicoletta
论文数: 0引用数: 0
h-index: 0
机构:
AORN Monaldi Cotugno CTO, Unita Operat Complessa Anat & Istol Patol, Naples, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
De Rosa, Nicoletta
Cavazza, Alberto
论文数: 0引用数: 0
h-index: 0
机构:
Azienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Cavazza, Alberto
Mengoli, Maria Cecilia
论文数: 0引用数: 0
h-index: 0
机构:
Azienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Mengoli, Maria Cecilia
Della Casa, Giovanni
论文数: 0引用数: 0
h-index: 0
机构:
Azienda Osped Policlin Univ Modena & Reggio Emili, Dept Diagnost Radiol, Modena, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Della Casa, Giovanni
Nannini, Nazarena
论文数: 0引用数: 0
h-index: 0
机构:
Univ Padua, Dept Cardiac Thorac & Vasc Sci, Padua, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Nannini, Nazarena
Colby, Thomas Vail
论文数: 0引用数: 0
h-index: 0
机构:
Mayo Clin Arizona, Dept Lab Med & Pathol, Scottsdale, AZ USAAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Numata, Yasunao
Sasaki, Shigeru
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Sasaki, Shigeru
Magara, Kazufumi
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Magara, Kazufumi
Takasawa, Akira
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Takasawa, Akira
Sugawara, Taro
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Surg Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Sugawara, Taro
Ohara, Naruki
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Ohara, Naruki
Akutsu, Noriyuki
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Akutsu, Noriyuki
Hasegawa, Tadashi
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Surg Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Hasegawa, Tadashi
Osanai, Makoto
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Osanai, Makoto
Nakase, Hiroshi
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
机构:
Department of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065Department of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065
Dogan S.
Barnes L.
论文数: 0引用数: 0
h-index: 0
机构:
Emeritus Professor of Pathology, University of Pittsburgh Medical Center, Presbyterian Hospital, Pittsburgh, PA 15213Department of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065
Barnes L.
Cruz-Vetrano W.P.
论文数: 0引用数: 0
h-index: 0
机构:
Laboratory Services, Altoona Regional Health System, AltoonaDepartment of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065
机构:
Azienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Rossi, Giulio
De Rosa, Nicoletta
论文数: 0引用数: 0
h-index: 0
机构:
AORN Monaldi Cotugno CTO, Unita Operat Complessa Anat & Istol Patol, Naples, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
De Rosa, Nicoletta
Cavazza, Alberto
论文数: 0引用数: 0
h-index: 0
机构:
Azienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Cavazza, Alberto
Mengoli, Maria Cecilia
论文数: 0引用数: 0
h-index: 0
机构:
Azienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Mengoli, Maria Cecilia
Della Casa, Giovanni
论文数: 0引用数: 0
h-index: 0
机构:
Azienda Osped Policlin Univ Modena & Reggio Emili, Dept Diagnost Radiol, Modena, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Della Casa, Giovanni
Nannini, Nazarena
论文数: 0引用数: 0
h-index: 0
机构:
Univ Padua, Dept Cardiac Thorac & Vasc Sci, Padua, ItalyAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
Nannini, Nazarena
Colby, Thomas Vail
论文数: 0引用数: 0
h-index: 0
机构:
Mayo Clin Arizona, Dept Lab Med & Pathol, Scottsdale, AZ USAAzienda Osped Arcispedale Santa Maria Nuova IRCCS, Unita Anat Patol, I-42123 Reggio Emilia, Italy
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Numata, Yasunao
Sasaki, Shigeru
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Sasaki, Shigeru
Magara, Kazufumi
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Magara, Kazufumi
Takasawa, Akira
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Takasawa, Akira
Sugawara, Taro
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Surg Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Sugawara, Taro
Ohara, Naruki
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Ohara, Naruki
Akutsu, Noriyuki
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Akutsu, Noriyuki
Hasegawa, Tadashi
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Surg Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Hasegawa, Tadashi
Osanai, Makoto
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Pathol, Sch Med, Sapporo, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
Osanai, Makoto
Nakase, Hiroshi
论文数: 0引用数: 0
h-index: 0
机构:
Sapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, JapanSapporo Med Univ, Dept Gastroenterol & Hepatol, Sch Med, Minami 1 Jo Nishi 16 Chome Chuo Ku, Sapporo 0608543, Japan
机构:
Department of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065Department of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065
Dogan S.
Barnes L.
论文数: 0引用数: 0
h-index: 0
机构:
Emeritus Professor of Pathology, University of Pittsburgh Medical Center, Presbyterian Hospital, Pittsburgh, PA 15213Department of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065
Barnes L.
Cruz-Vetrano W.P.
论文数: 0引用数: 0
h-index: 0
机构:
Laboratory Services, Altoona Regional Health System, AltoonaDepartment of Pathology, Memorial Sloan-Kettering Cancer Center, New York, NY 10065