Brown-Mclean syndrome in an aphakic patient with homocystinuria: The first reported case in Middle East

被引:1
作者
Alenezi, Saad H. [1 ,2 ]
Alrefaie, S. M. [2 ]
Alreshidi, Shaker O. [1 ,2 ]
ALBalawi, Hani B. [3 ]
Osorio, Hernan M. [2 ]
机构
[1] Majmaah Univ, Dept Ophthalmol, POB 66, Al Majmaah 11952, Saudi Arabia
[2] King Khalid Eye Specialist Hosp, Anterior Segment Div, Riyadh, Saudi Arabia
[3] Tabuk Univ, Dept Ophthalmol, Tabuk, Saudi Arabia
关键词
Brown-McLean syndrome; homocystinuria; peripheral corneal edema; subluxated lens;
D O I
10.4103/1319-4534.322619
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
Brown-McLean syndrome not reported in association with homocystinuria and generally occurs in patients with long-term aphakia. Presented as peripheral corneal edema with central clear cornea tends to spare vision without the need of any surgical intervention. The purpose of reporting such a rare condition as a first case of Brown-McLean syndrome associated with systemic disease of homocystinuria. Brown-McLean Syndrome in a patient with homocystinuria generally occurs in patients with long-term aphakia after different modalities of surgical intervention. A high clinical suspicion and regular follow-up is warranted for patients with systemic diseases who are aphakic or present with a subluxated lens for early intervention and better prognosis if needed.
引用
收藏
页码:300 / 302
页数:3
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