Hepatoblastoma with congenital absence of the portal vein - A case report

被引：28
作者：
Kawano, S.
Hasegawa, S.
Urushihara, N.
Okazaki, T.
Yoshida, A.
Kusafuka, J.
Mimaya, J.
Horikoshi, Y.
Aoki, K.
Hamazaki, M.
机构：
[1] Showa Univ, Fujigaoka Hosp, Dept Pediat Surg, Aoba Ku, Yokohama, Kanagawa 2278501, Japan
[2] Shizuoka Childrens Hosp, Dept Pediat Surg, Shizuoka, Japan
[3] Shizuoka Childrens Hosp, Dept Hematol Oncol, Shizuoka, Japan
[4] Shizuoka Childrens Hosp, Dept Radiol, Shizuoka, Japan
[5] Shizuoka Childrens Hosp, Dept Pathol, Shizuoka, Japan
来源：
EUROPEAN JOURNAL OF PEDIATRIC SURGERY | 2007年 / 17卷 / 04期
关键词：
hepatoblastoma; congenital absence of the portal vein; extremely-low-birth-weight infant;
D O I：
10.1055/s-2007-965448
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
A 17-month-old girl who had been followed up as an extremely-low-birth-weight infant presented with hepatoblastoma in the right lobe of her liver. Preoperative angiography revealed an absence of the portal vein, and the visceral venous return was through the left renal vein into the inferior vena cava. No liver dysfunction and no jaundice were found; however, a marked elevation of the alpha-fetoprotein level was noted. She underwent a typical right hepatic lobectomy successfully after chemotherapy and has no evidence of recurrence 6 months after surgery.
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收藏
页码：292 / 294
页数：3
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