Peripheral neuroblastic tumor of the kidney: case report and review of literature

被引：2

作者：

Moscheo, Carla ^{[1
,2
]}

Campari, Alessandro ^{[3
]}

Podda, Marta Giorgia ^{[1
]}

Riccipetitoni, Giovanna ^{[4
]}

Collini, Paola ^{[5
]}

Renne, Salvatore Lorenzo ^{[5
]}

Vella, Claudio ^{[4
]}

Napolitano, Marcello ^{[3
]}

Luksch, Roberto ^{[1
]}

机构：

[1] Fdn IRCCS Ist Nazl Tumori, Pediat Oncol Unit, Milan, Italy

[2] Meyer Childrens Univ Hosp, Dept Pediat Oncol, Neuro Oncol Unit, Viale Gaetano Pieraccini 24, I-50139 Florence, Italy

[3] V Buzzi Childrens Hosp, Dept Pediat Radiol, Milan, Italy

[4] Univ Milan, Childrens Hosp V Buzzi, Pediat Surg, Milan, Italy

[5] Fdn IRCCS Ist Nazl Tumori, Soft Tissue & Bone Pathol, Histopathol & Pediat Pathol Unit, Milan, Italy

来源：

TUMORI JOURNAL | 2018年 / 104卷 / 06期

关键词：

Ganglioneuroblastoma intermixed; kidney; pediatrics; WILMS;

D O I：

10.1177/0300891618788475

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Introduction: Peripheral neuroblastic tumors (PNTs) account for 8%-10% of all pediatric tumors. Adrenal glands and sympathetic ganglia are the commonest site of tumor growth. In the clinicopathologic spectrum of PNTs, neuroblastoma and ganglioneuroma are the most primitive and the most mature tumor form, while ganglioneuroblastoma represents an intermediate state of maturation. Surgical resection is the therapy of choice in localized disease, but can lead to serious complications when performed in the presence of certain imaging-defined risk factors. Case presentation: We present a rare case of primary intrarenal ganglioneuroblastoma diagnosed in a teenager who underwent conservative surgery and, despite this, developed upper pole renal ischemia without loss of parenchymal function. Conclusion: We underline the complex management of these extremely rare cases of neuroblastic tumors, which require a dedicated multidisciplinary team.

引用

页码：NP34 / NP37

页数：4