Ion channelopathies: a tapped-out mine?

被引:2
作者
Dudley, Samuel C., Jr. [1 ]
机构
[1] Univ Illinois, Jesse Brown VA Med Ctr, Cardiol Sect, Dept Med,Div Cardiol, Chicago, IL 60612 USA
来源
AMERICAN JOURNAL OF PHYSIOLOGY-HEART AND CIRCULATORY PHYSIOLOGY | 2011年 / 300卷 / 03期
关键词
LONG QT SYNDROME; POLYMORPHIC VENTRICULAR-TACHYCARDIA; CARDIAC-ARRHYTHMIA; BRUGADA-SYNDROME; MECHANISMS;
D O I
10.1152/ajpheart.01281.2010
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:H716 / H717
页数:2
相关论文
共 10 条
  • [1] MOLECULAR MECHANISM FOR AN INHERITED CARDIAC-ARRHYTHMIA
    BENNETT, PB
    YAZAWA, K
    MAKITA, N
    GEORGE, AL
    [J]. NATURE, 1995, 376 (6542) : 683 - 685
  • [2] Catecholaminergic polymorphic ventricular tachycardia: A paradigm to understand mechanisms of arrhythmias associated to impaired Ca2+ regulation
    Cerrone, Marina
    Napolitano, Carlo
    Priori, Silvia G.
    [J]. HEART RHYTHM, 2009, 6 (11) : 1652 - 1659
  • [3] A MOLECULAR-BASIS FOR CARDIAC-ARRHYTHMIA - HERG MUTATIONS CAUSE LONG QT SYNDROME
    CURRAN, ME
    SPLAWSKI, I
    TIMOTHY, KW
    VINCENT, GM
    GREEN, ED
    KEATING, MT
    [J]. CELL, 1995, 80 (05) : 795 - 803
  • [4] Y1767C, a novel SCN5A mutation, induces a persistent Na+ current and potentiates ranolazine inhibition of Nav1.5 channels
    Huang, Hai
    Priori, Silvia G.
    Napolitano, Carlo
    O'Leary, Michael E.
    Chahine, Mohamed
    [J]. AMERICAN JOURNAL OF PHYSIOLOGY-HEART AND CIRCULATORY PHYSIOLOGY, 2011, 300 (01): : H288 - H299
  • [5] Mechanisms and clinical management of inherited channelopathies: Long QT syndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia, and short QT syndrome
    Kaufman, Elizabeth S.
    [J]. HEART RHYTHM, 2009, 6 (08) : S51 - S55
  • [6] Cardiac Na+ Current Regulation by Pyridine Nucleotides
    Liu, Man
    Sanyal, Shamarendra
    Gao, Ge
    Gurung, Iman S.
    Zhu, Xiaodong
    Gaconnet, Georgia
    Kerchner, Laurie J.
    Shang, Lijuan L.
    Huang, Christopher L-H.
    Grace, Andrew
    London, Barry
    Dudley, Samuel C., Jr.
    [J]. CIRCULATION RESEARCH, 2009, 105 (08) : 737 - U39
  • [7] Genetics of acquired long QT syndrome
    Roden, DM
    Viswanathan, PC
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 2005, 115 (08) : 2025 - 2032
  • [8] Effects of sodium channel block with mexiletine to reverse action potential prolongation in in vitro models of the long QT syndrome
    Sicouri, S
    Antzelevitch, D
    Heilmann, C
    Antzelevitch, C
    [J]. JOURNAL OF CARDIOVASCULAR ELECTROPHYSIOLOGY, 1997, 8 (11) : 1280 - 1290
  • [9] Flecainide prevents catecholaminergic polymorphic ventricular tachycardia in mice and humans
    Watanabe, Hiroshi
    Chopra, Nagesh
    Laver, Derek
    Hwang, Hyun Seok
    Davies, Sean S.
    Roach, Daniel E.
    Duff, Henry J.
    Roden, Dan M.
    Wilde, Arthur A. M.
    Knollmann, Bjoern C.
    [J]. NATURE MEDICINE, 2009, 15 (04) : 380 - 383
  • [10] Cellular basis for the Brugada syndrome and other mechanisms of arrhythmogenesis associated with ST-segment elevation
    Yan, GX
    Antzelevitch, C
    [J]. CIRCULATION, 1999, 100 (15) : 1660 - 1666