Right ventricular biopsy findings of hypertrophic cardiomyopathy in a patient with Noonan syndrome

被引：3
作者：
Skinker, DM
Cottrill, CM
O'Connor, WN
机构：
[1] Univ Kentucky, Albert B Chandler Med Ctr, Dept Pathol, Lexington, KY 40536 USA
[2] Univ Kentucky, Albert B Chandler Med Ctr, Dept Pediat, Lexington, KY 40536 USA
来源：
CARDIOLOGY IN THE YOUNG | 1998年 / 8卷 / 02期
关键词：
hypertrophic cardiomyopathy; Noonan syndrome; cardiomyocyte disarray;
D O I：
10.1017/S104795110000620X
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
We report right ventricular ultrastructure in a 20-year-old patient with Noonan's Syndrome. Initial left ventricular and septal myocardial hypertrophy, observed at 2 months without obstruction, progressed to biventricular involvement over 18 years. Histopathologic evidence of cardiomyocytic disarray, with ultrastructural evidence of myofibrillar disarray, confirmed typical biopsy findings of hypertrophic cardiomyopathy on the right ventricular side of the septum.
引用
收藏
页码：256 / 259
页数：4
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