Hurler's syndrome with cor pulmonale secondary to obstructive sleep apnoea treated by continuous positive airway pressure

被引：21

作者：

Chan, D ^{[1
]}

Li, AM ^{[1
]}

Yam, MC ^{[1
]}

Li, CK ^{[1
]}

Fok, TF ^{[1
]}

机构：

[1] Chinese Univ Hong Kong, Prince Wales Hosp, Dept Paediat, Shatin, Hong Kong, Peoples R China

来源：

JOURNAL OF PAEDIATRICS AND CHILD HEALTH | 2003年 / 39卷 / 07期

关键词：

continuous positive airway pressure therapy; mucopolysaccharidosis; obstructive sleep apnoea syndrome;

D O I：

10.1046/j.1440-1754.2003.00218.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

A 6-year-old boy with Hurler's syndrome presented with right heart failure and pulmonary hypertension secondary to severe obstructive sleep apnoea. Both his sleep apnoea and cor pulmonale were effectively controlled with continuous positive airway pressure therapy.

引用

页码：558 / 559

页数：2

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