Nuss Procedure for pectus excavatum repair in a patient with osteogenesis imperfecta

被引：1

作者：

Lai, Krista ^{[1
]}

Padilla, Benjamin E. ^{[1
]}

Notrica, David M. ^{[1
,2
,3
,4
]}

机构：

[1] Phoenix Childrens Hosp, Div Pediat Surg, Phoenix, AZ USA

[2] Univ Arizona, Coll Med Phoenix, Phoenix, AZ USA

[3] Mayo Clin, Coll Med & Sci, Phoenix, AZ USA

[4] Phoenix Childrens Hosp, 1919 E Thomas Rd, Phoenix, AZ 85016 USA

来源：

JOURNAL OF PEDIATRIC SURGERY CASE REPORTS | 2022年 / 82卷

关键词：

Osteogenesis imperfecta; Pectus excavatum; Nuss; MIRPE;

D O I：

10.1016/j.epsc.2022.102311

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

A 17-year-old male with Osteogenesis Imperfecta (OI) type 1 and history of prior spinal instrumentation for kyphosis presented with severe symptomatic pectus excavatum (PEx). His Haller index was 6.7 with a Pectus Correction Index of 51%. He underwent uncomplicated Nuss procedure with insertion of 3 bars and complete repair of the PEx. A single sternal fracture was sustained during correction and healed without deformity. After two years, he developed leftsided pain and two of 3 bars were removed with maintained chest correction. This case report demonstrates the feasibility of Nuss procedure in adolescents with OI and outlines improvements to the technique in future patients with OI.

引用

页数：6

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