Prion disease

被引：12

作者：

Eggenberger, Eric ^{[1
]}

机构：

[1] Michigan State Univ, Dept Neurol & Ophthalmol, E Lansing, MI 48824 USA

来源：

NEUROLOGIC CLINICS | 2007年 / 25卷 / 03期

关键词：

D O I：

10.1016/j.ncl.2007.03.006

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Prion diseases are a unique group of neurologic diseases caused by an abnormal protein conformation. Prion diseases encompass genetic, sporadic, iatrogenic, and acquired conditions in humans and other mammals. Although they are relatively rare, they produce a diverse array of symptoms, uniformly are fatal, and provide important information about proteins and degenerative neurobiology in addition to lessons about animal and human food chains.

引用

页码：833 / +

页数：11

共 20 条

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