Systemic capillary leak syndrome: two cases report

被引：5

作者：

Sahnoun, I ^{[1
]}

Harmouche, H ^{[1
]}

Aouni, M ^{[1
]}

Mezalek, ZT ^{[1
]}

Adnaoui, M ^{[1
]}

Mohattane, H ^{[1
]}

Maaouni, A ^{[1
]}

机构：

[1] Hop Ibn Sina, Serv Med Interne, Rabat, Morocco

来源：

REVUE DE MEDECINE INTERNE | 2005年 / 26卷 / 05期

关键词：

severe hypovolemic chock; systemic capillary leak syndrome; capillary hyperpermeability; Clarkson syndrome; rhabdomyolysis;

D O I：

10.1016/j.revmed.2004.12.009

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Introduction. - Systemic capillary leak syndrome (SHCI) is a rare disease with poor prognosis, characterized by recurrent episodes of generalized edema and hypotension. Exegesis. - Two patients a 41 and 34-year-old woman were admitted with a generalized edema and several episode of shock. One patient had muscular edema with compartment syndrome imposing the aponevrotomia of discharge in emergency. The association of elevated hematocrit, decreased albumin serum concentration confirmed the diagnosis of SHCI. Administration of intravenous fluids improved the clinical and biological symptomatology. Conclusion. - These two new observations are comparable to the published cases. We didn't find dysalobulinemia whose existence is frequented. The treatment of shock requires macromolecules solutions. The preventive treatment remains empiric. (c) 2005 Elsevier SAS. Tons droits reserves.

引用

页码：409 / 414

页数：6

共 27 条

[1] Chronic systemic capillary leak syndrome. Report of a case and review of the literature [J].