Childhood vulval lichen sclerosus is a patient with ectodermal dysplasia and uncombable hair

被引：6

作者：

Powell, J ^{[1
]}

Wojnarowska, F ^{[1
]}

Dawber, R ^{[1
]}

Slavotinek, A ^{[1
]}

Huson, S ^{[1
]}

机构：

[1] Oxford Radcliffe Hosp, Dept Dermatol, Oxford OX3 7JL, England

来源：

PEDIATRIC DERMATOLOGY | 1998年 / 15卷 / 06期

关键词：

D O I：

10.1046/j.1525-1470.1998.1998015446.x

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

An 11-year-old girl was diagnosed as having ectodermal dysplasia, with abnormalities of her nails, teeth, and hair noted From infancy. Her hair was unruly and investigations confirmed the changes seen in "cheveux incoiffables"-the uncombable hair syndrome. She also had atopy requiring treatment to control asthma and eczema. When she was 8 years old she developed vulval lichen sclerosus, which was controlled easily with early treatment. The coexistence of these conditions is discussed.

引用

页码：446 / 449

页数：4

共 11 条

[1] Treatment of childhood vulvar lichen sclerosus with potent topical corticosteroid [J].

Fischer, G ;

Rogers, M .

PEDIATRIC DERMATOLOGY, 1997, 14 (03) :235-238

[2] LICHEN-SCLEROSUS-ET-ATROPHICUS IN CHILDREN MISDIAGNOSED AS SEXUAL ABUSE [J].

HANDFIELDJONES, SE ;

HINDE, FRJ ;

KENNEDY, CTC .

BRITISH MEDICAL JOURNAL, 1987, 294 (6584) :1404-1405

[3] AUTOSOMAL DOMINANT HYPODONTIA WITH NAIL DYSGENESIS - REPORT OF 29 CASES IN 6 FAMILIES [J].

HUDSON, CD ;

WITKOP, CJ .

ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTICS, 1975, 39 (03) :409-423

[4] CHEVEUX INCOIFFABLES - DIAGNOSTIC, CLINICAL AND HAIR MICROSCOPIC FINDINGS, AND PATHOGENIC STUDIES [J].

MALLON, E ;

DAWBER, RPR ;

DEBERKER, D ;

FERGUSON, DJP .

BRITISH JOURNAL OF DERMATOLOGY, 1994, 131 (05) :608-614

[5]

MARREN P, 1995, BRIT J DERMATOL, V132, P197

[6]

Marren P, 1995, BRIT J DERMATOL, V133, P21

[7] ECTODERMAL DYSPLASIAS - A CLINICAL CLASSIFICATION AND A CAUSAL REVIEW [J].

PINHEIRO, M ;

FREIREMAIA, N .

AMERICAN JOURNAL OF MEDICAL GENETICS, 1994, 53 (02) :153-162

[8]

Salinas C F, 1988, Birth Defects Orig Artic Ser, V24, P149

[9] UNCOMBABLE HAIR SYNDROME - OBSERVATIONS ON RESPONSE TO BIOTIN AND OCCURRENCE IN SIBLINGS WITH ECTODERMAL DYSPLASIA [J].

SHELLEY, WB ;

SHELLEY, ED .

JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1985, 13 (01) :97-102

[10]

SILENGO MC, 1982, CLIN GENET, V21, P297

← 1 2 →