Characteristics of hyperthermia and its complications in patients with Prader Willi syndrome

被引：17

作者：

Ince, E

Çiftçi, E

Tekin, M

Kendirli, T

Tutar, E

Dalgiç, N

Öncel, S

Dogru, Ü

机构：

[1] Ankara Univ, Sch Med, Dept Pediat, Div Pediat Infect Dis, Ankara, Turkey

[2] Ankara Univ, Sch Med, Dept Pediat, Div Genet, Ankara, Turkey

[3] Ankara Univ, Sch Med, Dept Pediat, Intens Care Unit, Ankara, Turkey

[4] Ankara Univ, Sch Med, Dept Pediat, Div Cardiol, Ankara, Turkey

来源：

PEDIATRICS INTERNATIONAL | 2005年 / 47卷 / 05期

关键词：

fever; hyperthermia; Prader-Willi syndrome; septic shock;

D O I：

10.1111/j.1442-200x.2005.02124.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Background: Thermoregulation problems, resulting in hypo- or hyperthermia, have been infrequently reported in children with Prader Willi syndrome (PWS), yet their clinical details remained unknown. Methods: The clinical characteristics of three infants with PWS are reported. Results: Etiologies of high fever could not be identified in three children with PWS. One of these children was also admitted to the intensive care unit with extremely high body temperature in a life-threatening condition, similar to septic shock, without a plausible explanation. Conclusion: Hyperthermia may be a part of the clinical spectrum in young infants with PWS and should be carefully monitored, since it may cause life-threatening complications.

引用

页码：550 / 553

页数：4

共 12 条

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CASSIDY SB, 1991, AM J MED GENET, V41, P528

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CASSIDY SB, 2001, MANAGEMENT GENETIC S, P301

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