Budd-Chiari syndrome caused by hepatic vein thrombosis in a patient with myeloproliferative disorder

被引：5

作者：

Usui, T ^{[1
]}

Kitano, K ^{[1
]}

Midorikawa, T ^{[1
]}

Yoshizawa, K ^{[1
]}

Kobayashi, H ^{[1
]}

Tanaka, E ^{[1
]}

Matsunami, H ^{[1
]}

Kawasaki, S ^{[1
]}

Kiyosawa, K ^{[1
]}

机构：

[1] SHINSHU UNIV,SCH MED,DEPT INTERNAL MED 2,MATSUMOTO,NAGANO 390,JAPAN

来源：

INTERNAL MEDICINE | 1996年 / 35卷 / 11期

关键词：

latent myeloproliferative disorder; liver transplantation;

D O I：

10.2169/internalmedicine.35.871

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We report a 24-year-old Japanese female hospitalized with jaundice and ascites. She exhibited hepatosplenomegaly, severe liver dysfunction, and slight polycythemia with an increase in serum levels of beta-thromboglobin and platelet factor 4. Bone marrow was hypercellular with an increase in progenitor cells. The aggregation response of platelets to ADP and to collagen was markedly increased. Venography revealed narrowed hepatic veins with 'spider web' sign. Liver biopsy revealed hepatic congestion. Budd-Chiari syndrome was diagnosed, and was thought to be due to thrombosis related to myeloproliferative disorder. Liver transplant was successful in relieving symptoms.

引用

页码：871 / 875

页数：5