Mitochondrial encephalomyopathy (Kearns-Sayre syndrome) with complete atrioventricular block - A case report

被引：4
作者：
Kakura, H
Tachibana, Y
Nakamura, K
Tanaka, Y
Sanada, J
Arima, T
机构：
[1] Kagoshima Univ, Fac Med, Dept Internal Med 2, Kagoshima 890, Japan
[2] Natl So Kyu Syu Cent Hosp, Cardiovasc Div 2, Kagoshima, Japan
来源：
JAPANESE CIRCULATION JOURNAL-ENGLISH EDITION | 1998年 / 62卷 / 08期
关键词：
complete atrioventricular block; DDD mode pacemaker; Kearns-Sayre syndrome; stage of implantation;
D O I：
10.1253/jcj.62.623
中图分类号：
N09 [自然科学史]; B [哲学、宗教];
学科分类号：
01 ; 0101 ; 010108 ; 060207 ; 060305 ; 0712 ;
摘要：
A pacemaker was implanted into a 17-year-old man with cardiac failure due to complete atrioventricular block complicated by mitochondrial encephalomyopathy (Kearns-Sayre syndrome). Due to the possible complication of latent myocardial dysfunction, it was decided to implant the dual chamber pacemaker (DDD) and the operation mode was set to DDD 70 ppm 1 year after implantation; this alleviated the cardiac failure. In this case, the necessity of preventive pacemaker implantation in the early stage of cardiac failure was recognized.
引用
收藏
页码：623 / 625
页数：3
相关论文
共 11 条
  • [1] CARDIAC INVOLVEMENT IN MITOCHONDRIAL DISEASES - A STUDY ON 17 PATIENTS WITH DOCUMENTED MITOCHONDRIAL-DNA DEFECTS
    ANAN, R
    NAKAGAWA, M
    MIYATA, M
    HIGUCHI, I
    NAKAO, S
    SUEHARA, M
    OSAME, M
    TANAKA, H
    [J]. CIRCULATION, 1995, 91 (04) : 955 - 961
  • [2] LUMPING OR SPLITTING - OPHTHALMOPLEGIA-PLUS OR KEARNS-SAYRE SYNDROME
    BERENBERG, RA
    PELLOCK, JM
    DIMAURO, S
    SCHOTLAND, DL
    BONILLA, E
    EASTWOOD, A
    HAYS, A
    VICALE, CT
    BEHRENS, M
    CHUTORIAN, A
    ROWLAND, LP
    [J]. ANNALS OF NEUROLOGY, 1977, 1 (01) : 37 - 54
  • [3] CHANNER KS, 1988, BRIT HEART J, V59, P486
  • [4] MYOCARDIAL ULTRASTRUCTURE AND THE DEVELOPMENT OF ATRIOVENTRICULAR-BLOCK IN KEARNS-SAYRE SYNDROME
    CHARLES, R
    HOLT, S
    KAY, JM
    EPSTEIN, EJ
    REES, JR
    [J]. CIRCULATION, 1981, 63 (01) : 214 - 219
  • [5] RETINITIS PIGMENTOSA, EXTERNAL OPHTHALMOPLEGIA, AND COMPLETE HEART BLOCK - UNUSUAL SYNDROME WITH HISTOLOGIC STUDY IN ONE OF 2 CASES
    KEARNS, TP
    SAYRE, GP
    [J]. ARCHIVES OF OPHTHALMOLOGY, 1958, 60 (02) : 280 - 289
  • [6] KEARNS-SAYRE SYNDROME IN THE ELDERLY - MITOCHONDRIAL MYOPATHY WITH ADVANCED HEART-BLOCK
    KENNY, D
    WETHERBEE, J
    [J]. AMERICAN HEART JOURNAL, 1990, 120 (02) : 440 - 443
  • [7] MATUSHIMA S, 1990, THER RES, V11, P129
  • [8] MORI K, 1991, ACTA CARDIOL PAEDIAT, V7, P436
  • [9] NAMBA H, 1994, CARDIAC PACING ELECT, V10, P155
  • [10] INDICATIONS FOR PACEMAKER IMPLANTATION IN THE KEARNS-SAYRE SYNDROME
    POLAK, PE
    ZIJLSTRA, F
    ROELANDT, JRTC
    [J]. EUROPEAN HEART JOURNAL, 1989, 10 (03) : 281 - 282
12