Langerhans cell histiocytosis in an adult patient associated with sclerosing cholangitis and cerebellar atrophy

被引：8

作者：

Desrame, J

Béchade, D

Defuentes, G

Goasdoue, P

Raynaud, JJ

Claude, V

Renard, JL

Genereau, T

Coutant, G

Algayres, JP

机构：

[1] Hop Instruct Armees Val Grace, Med Clin, F-75005 Paris, France

[2] Hop Instruct Armees Val Grace, Serv Imagerie Med, F-75005 Paris, France

[3] Hop Instruct Armees Val Grace, Neurol Clin, F-75005 Paris, France

[4] Hop Instruct Armees Begin, Serv Anat Pathol, F-00498 Paris, France

[5] Hop St Antoine, Serv Med Interne, F-75012 Paris, France

来源：

GASTROENTEROLOGIE CLINIQUE ET BIOLOGIQUE | 2005年 / 29卷 / 03期

关键词：

D O I：

10.1016/S0399-8320(05)80767-5

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

Langerhans' cell histiocytosis is a disorder in children or young adults, characterized by clonal proliferation of histiocytic cells, staining for CDIa, with uni or multifacal argon involvement. It's a rare condition in adults. We report a case of Langerhans' cell histiocytosis in an adult with sclerosing cholangitis which rapidly progressed to fatal liver failure and progressive cerebellar atrophy. Langerhans cell histiocytosis is a rare cause of sclerosing cholangititis in adults.

引用

页码：300 / 303

页数：4

共 22 条

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