Langerhans cell histiocytosis in an adult patient associated with sclerosing cholangitis and cerebellar atrophy

被引：8
作者：
Desrame, J
Béchade, D
Defuentes, G
Goasdoue, P
Raynaud, JJ
Claude, V
Renard, JL
Genereau, T
Coutant, G
Algayres, JP
机构：
[1] Hop Instruct Armees Val Grace, Med Clin, F-75005 Paris, France
[2] Hop Instruct Armees Val Grace, Serv Imagerie Med, F-75005 Paris, France
[3] Hop Instruct Armees Val Grace, Neurol Clin, F-75005 Paris, France
[4] Hop Instruct Armees Begin, Serv Anat Pathol, F-00498 Paris, France
[5] Hop St Antoine, Serv Med Interne, F-75012 Paris, France
来源：
GASTROENTEROLOGIE CLINIQUE ET BIOLOGIQUE | 2005年 / 29卷 / 03期
关键词：
D O I：
10.1016/S0399-8320(05)80767-5
中图分类号：
R57 [消化系及腹部疾病];
学科分类号：
摘要：
Langerhans' cell histiocytosis is a disorder in children or young adults, characterized by clonal proliferation of histiocytic cells, staining for CDIa, with uni or multifacal argon involvement. It's a rare condition in adults. We report a case of Langerhans' cell histiocytosis in an adult with sclerosing cholangitis which rapidly progressed to fatal liver failure and progressive cerebellar atrophy. Langerhans cell histiocytosis is a rare cause of sclerosing cholangititis in adults.
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页码：300 / 303
页数：4
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