Langerhans cell histiocytosis in an adult patient associated with sclerosing cholangitis and cerebellar atrophy

被引:8
作者
Desrame, J
Béchade, D
Defuentes, G
Goasdoue, P
Raynaud, JJ
Claude, V
Renard, JL
Genereau, T
Coutant, G
Algayres, JP
机构
[1] Hop Instruct Armees Val Grace, Med Clin, F-75005 Paris, France
[2] Hop Instruct Armees Val Grace, Serv Imagerie Med, F-75005 Paris, France
[3] Hop Instruct Armees Val Grace, Neurol Clin, F-75005 Paris, France
[4] Hop Instruct Armees Begin, Serv Anat Pathol, F-00498 Paris, France
[5] Hop St Antoine, Serv Med Interne, F-75012 Paris, France
来源
GASTROENTEROLOGIE CLINIQUE ET BIOLOGIQUE | 2005年 / 29卷 / 03期
关键词
D O I
10.1016/S0399-8320(05)80767-5
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Langerhans' cell histiocytosis is a disorder in children or young adults, characterized by clonal proliferation of histiocytic cells, staining for CDIa, with uni or multifacal argon involvement. It's a rare condition in adults. We report a case of Langerhans' cell histiocytosis in an adult with sclerosing cholangitis which rapidly progressed to fatal liver failure and progressive cerebellar atrophy. Langerhans cell histiocytosis is a rare cause of sclerosing cholangititis in adults.
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页码:300 / 303
页数:4
相关论文
共 22 条
[1]   Cholestasis, sclerosing cholangitis, and liver transplantation in Langerhans cell histiocytosis [J].
Braier, J ;
Ciocca, M ;
Latella, A ;
de Davila, MG ;
Drajer, M ;
Imventarza, O .
MEDICAL AND PEDIATRIC ONCOLOGY, 2002, 38 (03) :178-182
[2]   Langerhans cell histiocytosis: Retrospective evaluation of 123 patients at a single institution [J].
Braier, J ;
Chantada, G ;
Rosso, D ;
Bernaldez, P ;
Amaral, D ;
Latella, A ;
Balancini, B ;
Masautis, A ;
Goldberg, J .
PEDIATRIC HEMATOLOGY AND ONCOLOGY, 1999, 16 (05) :377-385
[3]  
Chazouillères O, 2003, GASTROEN CLIN BIOL, V27, P307
[4]   Recurrence of Langerhans cell histiocytosis in the graft after liver transplantation in adults [J].
de Diego, A ;
Escudero, M ;
Catalina, MV ;
Salcedo, M ;
Sánchez, AG ;
Alvarez, E ;
Clemente, G .
TRANSPLANTATION PROCEEDINGS, 2002, 34 (04) :1245-1247
[5]   LANGERHANS HISTIOCYTOSIS OF THE CHOLEDOCHUS IN AN ADULT PATIENT WITH A HISTORY OF DISSEMINATED DISEASE [J].
DIPALO, S ;
FARAVELLI, A ;
BERETTA, E ;
TACCAGNI, GL .
TUMORI, 1988, 74 (05) :593-597
[6]  
Donadieu J, 1996, ARCH DIS CHILD, V75, P17
[7]  
DONADIEU J, 1996, MED THERAPEUTIQUE, V2, P441
[8]   Histiocytosis: Recent physiopathological data [J].
Emile, JF ;
Brousse, N .
REVUE DE MEDECINE INTERNE, 1996, 17 (11) :891-892
[9]   MR OF INTRACRANIAL LANGERHANS CELL HISTIOCYTOSIS [J].
GEORGE, JC ;
EDWARDS, MK ;
SMITH, RR ;
PROVISOR, AJ .
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1994, 18 (02) :295-297
[10]   PROGRESSIVE SPINOCEREBELLAR DEGENERATION PLUS ASSOCIATED WITH LANGERHANS CELL HISTIOCYTOSIS - A NEW PARANEOPLASTIC-SYNDROME [J].
GOLDBERGSTERN, H ;
WEITZ, R ;
ZAIZOV, R ;
GORNISH, M ;
GADOTH, N .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1995, 58 (02) :180-183