Persistent Mullerian duct syndrome presenting with bilateral intra-abdominal gonadal tumours and obstructive uropathy

被引：6

作者：

Asthana, S ^{[1
]}

Deo, SV ^{[1
]}

Shukla, NK ^{[1
]}

Raina, V ^{[1
]}

Kumar, L ^{[1
]}

机构：

[1] All India Inst Med Sci, Inst Rotary Canc Hosp, New Delhi, India

来源：

CLINICAL ONCOLOGY | 2001年 / 13卷 / 04期

关键词：

persistent Mullerian duct syndrome; testicular tumour;

D O I：

10.1053/clon.2001.9275

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Persistent Mullerian duct syndrome is a rare, autosomal recessive intersex disorder characterized by the presence of completely developed Mullerian duct derivatives in an otherwise normally virilized mate with a 46, XY karyotype. We discuss a rare presentation of this disorder, bilateral gonadal tumours with obstructive uropathy, and its management, together,with a review of the literature.

引用

页码：304 / 306

页数：3

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