Primary spinal atypical teratoid/rhabdoid tumor (AT/RT) is extremely rare. A 9-month-old boy presented with tetraparesis. Subsequent MRI showed an intradural extramedullary bulky mass extending from C4 to T6. Subtotal removal of the tumor was performed and spinal AT/RT was proven histologically. Despite chemotherapy and radiation therapy, leptomeningeal dissemination was found on follow-up MRI. The patient died 20 months after his initial symptoms. We describe the MRI findings of this case and review the literature describing this rare disease.
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Gen PLA Hosp, Dept Pathol, Beijing, Peoples R China
China Aerosp Corp, Dept Pathol, Cent Hosp, Beijing, Peoples R ChinaGen PLA Hosp, Dept Pathol, Beijing, Peoples R China
Li, Fang
Gui, Qiuping
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Gen PLA Hosp, Dept Pathol, Beijing, Peoples R ChinaGen PLA Hosp, Dept Pathol, Beijing, Peoples R China
Gui, Qiuping
Piao, Yueshan
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Capital Med Univ, Xuanwu Hosp, Dept Pathol, Beijing, Peoples R ChinaGen PLA Hosp, Dept Pathol, Beijing, Peoples R China
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Juntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, JapanJuntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, Japan
Yaguchi, Akinori
Fujimura, Junya
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Juntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, JapanJuntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, Japan
Fujimura, Junya
Maruyama, Kazutaka
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Juntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, JapanJuntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, Japan
Maruyama, Kazutaka
Fujiwara, Megumi
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Juntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, JapanJuntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, Japan
Fujiwara, Megumi
Ishibashi, Takeshi
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Juntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, JapanJuntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, Japan
Ishibashi, Takeshi
Tomita, Osamu
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Juntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, JapanJuntendo Univ, Fac Med, Dept Pediat, 2-1-1 Hongo,Bunkyo Ku, Tokyo 1138421, Japan