Unusual variant of scimitar syndrome associated with an absent right pulmonary artery, stenosis of the inferior vena cava, hemi-azygous continuation and the VACTERL association

被引：4

作者：

Takawira, Farirai F. ^{[1
]}

Omar, Fareed

机构：

[1] Univ Pretoria, Steve Biko Acad Hosp, ZA-0002 Pretoria, South Africa

来源：

CARDIOVASCULAR JOURNAL OF AFRICA | 2013年 / 24卷 / 03期

关键词：

scimitar syndrome; absent pulmonary artery; hemi-azygous; stenosis; inferior vena cava; VACTERL association;

D O I：

10.5830/CVJA-2012-079

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We report on a two-month-old infant with an unusual form of scimitar syndrome, associated with an absent right pulmonary artery, obstructed inferior vena cava, hemi-azygous continuation and the VACTERL association. The infant posed a major management problem and eventually died from a lower respiratory tract infection.

引用

页码：E3 / E6

页数：4

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