Malignant Peripheral Nerve Sheath Tumour of Cervical Plexus - a Case Report

Malignant peripheral nerve sheath tumours are rare neoplasms, especially in the head and neck. They are often asymptomatic. We present a case of 29-years old patient with neurofibromatosis type 1 with malignant tumour of the cervical plexus. A small resistance in the upper mediastinum was diagnosed (ganglioneurinoma) in 2005 and treated surgically (total exstirpation). A small infiltration in the right supraclavicular area occurred five years later and was also managed surgically (debulking) - histologically MPNST. There was a relapse of this tumour in the same area in 2011; this was treated by en bloc resection, followed by chemotheraphy. At present, the patient is in a good clinical status, with no neurological deficit.