Surgical Treatment of Cardiovascular Complications in Patients with Marfan Syndrome: a Report of two Cases and Literature Review

被引：0

作者：

Bruls, S. ^{[1
]}

Radermecker, M. A. ^{[2
]}

Creemers, E. ^{[1
]}

Bonnet, P. ^{[2
]}

Nellessen, E. ^{[3
]}

Van Damme, H. ^{[1
]}

De Leval, L. ^{[4
]}

Defraigne, J. O. ^{[1
]}

机构：

[1] Univ Hosp Liege, Dept Cardiothorac Surg, B-4000 Liege, Belgium

[2] Univ Hosp Liege, Dept Human Anat, B-4000 Liege, Belgium

[3] Univ Hosp Liege, Dept Cardiol, B-4000 Liege, Belgium

[4] Univ Hosp Liege, Dept Pathol, B-4000 Liege, Belgium

来源：

ACTA CHIRURGICA BELGICA | 2012年 / 112卷 / 03期

关键词：

AORTIC ROOT REPLACEMENT; VALSALVA ANEURYSM; VALVE; SINUS; OPERATIONS; SURGERY; MANAGEMENT; REPAIR; RISK;

D O I：

暂无

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Cardiovascular disease is the main cause of morbidity and mortality in patients with Marfan syndrome. The most life threatening complication is aortic root aneurysms leading to aortic dissection or rupture. It can be prevented by regular aortic follow-up and prophylactic aortic surgery. Modern aortic surgery has led to a substantial increase in the life expectancy of these patients. We report two cases of Marfan syndrome with cardiovascular complications. Their management is discussed according to the most recent literature.

引用

页码：213 / 218

页数：6

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