Management of Pentalogy of Cantrell with complete ectopia cordis and Double Outlet Right Ventricle

被引：4

作者：

Harring, Gesa ^{[1
]}

Weil, Jochen ^{[1
]}

Thiel, Christian ^{[1
]}

Schmelzle, Rainer ^{[2
]}

Mueller, Goetz C. ^{[1
]}

机构：

[1] Univ Heart Ctr Hamburg, Dept Pediat Cardiol, Hamburg, Germany

[2] Univ Hosp Hamburg Eppendorf, Dept Oral & Maxillofacial, Hamburg, Germany

来源：

CONGENITAL ANOMALIES | 2015年 / 55卷 / 02期

关键词：

congenital heart disease; double outlet right ventricle; ectopia cordis; Pentalogy of Cantrell; CHEST-WALL RECONSTRUCTION;

D O I：

10.1111/cga.12096

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Pentalogy of Cantrell (PoC) is a rare congenital midline defect. We present a case and its treatment of PoC with complete ectopia cordis and congenital heart disease. Postnatally the congenital heart defect was surgically corrected and the ectopic heart was covered by musculous mobilized flap. Due to cephalic orientation of the heart and limited intrathoracic space, replacement of the heart into the thoracic cavity was initially not performed. After 11 years of follow up our patient now is without relevant limitations solely wearing a thoracic shelter. This case elucidates the complexity of further management. The potential risk of disastrous hemodynamic compromise by intrathoracic shift is to compare with the limited safety of the ectopic heart.

引用

页码：121 / 123

页数：3

共 6 条

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