Progressive encephalomyelitis with rigidity responsive to plasmapheresis and immunosuppression

被引：23
作者：
Fogan, L
机构：
[1] Department of Neurology, Kaiser Permanente Medical Center, Panorama City, CA
[2] Department of Neurology, Kaiser Permanente Medical Center, Panorama City, CA 94102-5497
来源：
ANNALS OF NEUROLOGY | 1996年 / 40卷 / 03期
关键词：
D O I：
10.1002/ana.410400315
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
The stiff-man syndrome is reported in a 55-year-old woman who also had signs of severe bulbar musculature hypercontraction. These clinical features correspond to the progressive encephalomyelitis with rigidity syndrome. Diazepam was minimally beneficial, but after treatment with plasmapheresis and corticosteroids, she was still asymptomatic when seen 5 years later.
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页码：451 / 453
页数：3
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