Airway Clearance Techniques for Primary Ciliary Dyskinesia; is the Cystic Fibrosis literature portable?

被引：27

作者：

Schofield, Lynne Marie ^{[1
]}

Duff, Alistair ^{[1
]}

Brennan, Cathy ^{[2
]}

机构：

[1] Leeds Gen Infirm, Leeds Teaching Hosp, Great George St, Leeds LS1 3EX, W Yorkshire, England

[2] Univ Leeds, Leeds Inst Hlth Sci, Leeds, W Yorkshire, England

来源：

PAEDIATRIC RESPIRATORY REVIEWS | 2018年 / 25卷

关键词：

PCD; Chest Physiotherapy; Airway Clearance; CF; KARTAGENERS-SYNDROME; EUROPEAN CHILDREN; PHYSIOTHERAPY; RECOMMENDATIONS; MANAGEMENT; CONSENSUS; INFANTS; QUALITY; COHORT; DNASE;

D O I：

10.1016/j.prrv.2017.03.011

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Primary Ciliary Dyskinesia (PCD) is a rare inherited disease with impaired mucociliary clearance. Airway clearance techniques (ACTs) are commonly recommended for patients with PCD to facilitate mucus clearance, despite a lack of evidence in this group. Current physiotherapy practice in PCD is based on evidence extrapolated from the field of Cystic Fibrosis (CF). This paper focuses on the available evidence and outlines challenges in extrapolating evidence between the conditions for best clinical practice. (C) 2017 Published by Elsevier Ltd.

引用

页码：73 / 77

页数：5

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