Left ventricular noncompaction is a genetic disorder that is thought to be related to an arrest in endomyocardial development. It is characterized by the presence of a prominent trabecular meshwork and deep recesses. In order to better characterize this recently described disorder, whose prognosis remains unclear, we review eight cases diagnosed at our hospital, describing their clinical, electrocardiographic and echocardiographic features as well as therapy and follow-up. We also discuss the most relevant data from the literature concerning pathogenesis, clinical presentation, diagnostic criteria, therapy and prognosis.
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Univ Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
Fleury Med & Saude, Sao Paulo, SP, BrazilUniv Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
Hotta, Viviane Tiemi
Tendolo, Sabrina Cunha
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Fleury Med & Saude, Sao Paulo, SP, BrazilUniv Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
Tendolo, Sabrina Cunha
Tude Rodrigues, Ana Clara
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Univ Sao Paulo, Fac Med, Hosp Clin, Sao Paulo, SP, Brazil
Hosp Israelita Albert Einstein, Sao Paulo, SP, BrazilUniv Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
Tude Rodrigues, Ana Clara
Fernandes, Fabio
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Fleury Med & Saude, Sao Paulo, SP, BrazilUniv Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
Fernandes, Fabio
Nastari, Luciano
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Fleury Med & Saude, Sao Paulo, SP, BrazilUniv Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
Nastari, Luciano
Mady, Charles
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Fleury Med & Saude, Sao Paulo, SP, BrazilUniv Sao Paulo, Fac Med, Hosp Clin, Inst Coracao InCor, Sao Paulo, SP, Brazil
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E Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USAE Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USA
Ilyas, Sadaf
Ganote, Charles
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E Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USAE Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USA
Ganote, Charles
Lajoie, Dawn
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E Tennessee State Univ, Quillen Coll Med, WLJ Forens Ctr, Div Forens Pathol,Dept Pathol, Johnson City, TN 37614 USAE Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USA
Lajoie, Dawn
Robertson, Julie
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Johnson City Med Ctr, Dept Pathol, Johnson City, TN USAE Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USA
Robertson, Julie
Cline-Parhamovich, Karen
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E Tennessee State Univ, Quillen Coll Med, WLJ Forens Ctr, Div Forens Pathol,Dept Pathol, Johnson City, TN 37614 USAE Tennessee State Univ, Quillen Coll Med, Dept Pathol, Johnson City, TN 37614 USA
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Amur State Med Acad, Cardiac Surg Clin, Blagoveshchensk, Russia
Amur State Med Acad, Cardiac Surg Clin, St Gorky 97, Blagoveshchensk 675001, RussiaAmur State Med Acad, Cardiac Surg Clin, Blagoveshchensk, Russia
Korotkikh, A., V
Vakhnenko, Yulia Vladimirovna
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Amur State Med Acad, Dept Hosp therapy course pharmacol, Blagoveshchensk, RussiaAmur State Med Acad, Cardiac Surg Clin, Blagoveshchensk, Russia
Vakhnenko, Yulia Vladimirovna
Zabolotskikh, Tatyana
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Amur State Med Acad, Blagoveshchensk, RussiaAmur State Med Acad, Cardiac Surg Clin, Blagoveshchensk, Russia
Zabolotskikh, Tatyana
Kazantsev, Anton Nikolaevich
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Kostroma Reg Hosp, Vasc Dept, Kostroma, RussiaAmur State Med Acad, Cardiac Surg Clin, Blagoveshchensk, Russia
Kazantsev, Anton Nikolaevich
Annaev, Zinat Shavkatovich
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Novyy Urengoy Cent Hosp, Neurosurg Dept, Novyy Urengoy, RussiaAmur State Med Acad, Cardiac Surg Clin, Blagoveshchensk, Russia