Noncompaction cardiomyopathy - A review of eight cases

被引:0
|
作者
Toste, Alexandra [1 ]
Branco, Luisa Moura [1 ]
Galrinho, Ana [1 ]
Lousinha, Ana [1 ]
Fiarresga, Antosio [1 ]
Oliveira, Mario M. [1 ]
Abreu, Joao [1 ]
Mendes, Joao Joao [1 ]
Ferreira, Lurdes [1 ]
Leal, Ana [1 ]
Ferreira, Rui Cruz [1 ]
机构
[1] Hosp Santa Marta, Serv Cardiol, Lisbon, Portugal
关键词
Left ventricular noncompaction; Cardiomyopathy; Doppler echocardiography; Heart failure; Diagnosis; Therapy; Prognosis;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Left ventricular noncompaction is a genetic disorder that is thought to be related to an arrest in endomyocardial development. It is characterized by the presence of a prominent trabecular meshwork and deep recesses. In order to better characterize this recently described disorder, whose prognosis remains unclear, we review eight cases diagnosed at our hospital, describing their clinical, electrocardiographic and echocardiographic features as well as therapy and follow-up. We also discuss the most relevant data from the literature concerning pathogenesis, clinical presentation, diagnostic criteria, therapy and prognosis.
引用
收藏
页码:1847 / 1864
页数:18
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