Vein of Galen aneurysmal malformation in a neonate presenting with congestive heart failure

Vein of Galen aneurysmal malformation is a rare complex vascular malformation that is characterized by arterial shunting into the median prosencephalic vein of Markowski, the embryonic precursor of the Galen vein. It occurs in less than 0.004% of deliveries. The disorder is classified as choroidal, mural, and mixed types. In most cases, it can be correctly diagnosed by prenatal ultrasonography performed in the third trimester. Herein, we present a case of choroidal VGAM who had not been evaluated by prenatal US, presented with severe heart failure in the early neonatal period, and died during the first days of life because of circulatory impairment.