Peritoneovenous shunting for intractable chylous ascites complicated with lymphangioleiomyomatosis

被引：20

作者：

Makino, Yuko ^{[1
]}

Shimanuki, Yuri ^{[1
]}

Fujiwara, Noriko ^{[2
]}

Morio, Yoshiteru ^{[1
]}

Sato, Koichi ^{[1
]}

Yoshimoto, Jiro ^{[2
]}

Gunji, Yoko ^{[1
]}

Suzuki, Tsutomu ^{[1
]}

Sasaki, Shin-ichi ^{[3
]}

Iwase, Akihiko ^{[4
]}

Kawasaki, Seiji ^{[2
]}

Takahashi, Kazuhisa ^{[1
]}

Seyama, Kuniaki ^{[1
]}

机构：

[1] Juntendo Univ, Sch Med, Dept Resp Med, Tokyo 113, Japan

[2] Juntendo Univ, Sch Med, Dept Hepatobiliary Pancreatosurg, Tokyo 113, Japan

[3] Urayasu Juntendo Univ Hosp, Div Internal Med 1, Urayasu, Japan

[4] Tokyo Metropolitan Koto Geriatr Med Ctr, Dept Resp Med, Tokyo, Japan

来源：

INTERNAL MEDICINE | 2008年 / 47卷 / 04期

关键词：

tumor suppressor gene syndrome; the TSC genes; lymphangioleiomyoma;

D O I：

10.2169/internalmedicine.47.0475

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 38-year-old woman was admitted due to lymphangioleiomyomatosis (LAM)-associated massive chylous ascites and progressive cachexia. She was incidentally diagnosed to have ascites during her regular physical check-up two years previously and LAM was revealed as its underlying cause. Periodic paracentesis was required to ameliorate ascites-associated symptoms, but resulted in lymphocytopenia, malnutrition, and deterioration of general status. Ascites was refractory to diuretics and fat-restricted diet. Peritoneovenous shunt (Denver shunt.) was placed and thereafter ascites has been managed successfully without any complications for one year after the placement. Peritoneovenous shunt should be considered in LAM patients whose chylous ascites can not be managed with conservative treatments.

引用

页码：281 / 285

页数：5

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