Outcomes in Hypoplastic Left Heart Syndrome

被引：37

作者：

Metcalf, Meghan Kiley ^{[1
,2
]}

Rychik, Jack ^{[1
,2
]}

机构：

[1] Childrens Hosp Philadelphia, Div Cardiol, 3401 Civ Ctr Blvd, Philadelphia, PA 19104 USA

[2] Univ Penn, Dept Pediat, Perelman Sch Med, Philadelphia, PA 19104 USA

来源：

PEDIATRIC CLINICS OF NORTH AMERICA | 2020年 / 67卷 / 05期

关键词：

Hypoplastic left heart syndrome; Outcomes for congenital heart disease; Congenital heart surgery; Fetal echocardiography; Neurocognitive deficits in congenital heart disease; PROTEIN-LOSING ENTEROPATHY; SINGLE-VENTRICLE; NEURODEVELOPMENTAL OUTCOMES; FENESTRATED FONTAN; NORWOOD PROCEDURE; EARLY REDUCTION; ATRIAL SEPTUM; RISK-FACTORS; VOLUME WORK; SURVIVAL;

D O I：

10.1016/j.pcl.2020.06.008

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Hypoplastic left heart syndrome (HLHS) is a complex form of congenital heart disease defined by anatomic and functional inadequacy of the left side of the heart with nonviability of the left ventricle to perform systemic perfusion. Lethal if not treated, a strategy for survival currently is well established, with continuing improvement in outcomes over the past 30 years. Prenatal diagnosis, good newborn care, improved surgical skills, specialized postoperative care, and unique strategies for interstage monitoring all have contributed to increasing likelihood of survival. The unique life with a single right ventricle and a Fontan circulation is a focused area of investigation. © 2020 Elsevier Inc.

引用

页码：945 / 962

页数：18

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