Hepatocellular carcinoma in a patient with hereditary hemochromatosis and noncirrhotic liver.: A case report

被引:0
作者
Köhler, HH
Höhler, T
Küsel, U
Kirkpatrick, CJ
Schirmacher, P
机构
[1] Univ Mainz, Inst Pathol, D-55131 Mainz, Germany
[2] Univ Mainz, Dept Internal Med 1, D-55131 Mainz, Germany
[3] Univ Mainz, Dept Transplantat Surg, D-55131 Mainz, Germany
关键词
hepatocellular carcinoma; hereditary hemachromatosis; noncirrhotic liver;
D O I
暂无
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
A case of a 62-year-old patient with hereditary hemochromatosis is reported, who developed hepatocellular carcinoma (HCC) in the absence of cirrhosis and other potential risk factors for HCC. Occurrence of HCC in patients with genetic hemochromatosis and noncirrhotic liver is a rare event which has previously been described only six times and appears to be limited to male patients.
引用
收藏
页码:509 / 513
页数:5
相关论文
共 25 条
  • [1] VALUE OF HEPATIC IRON MEASUREMENTS IN EARLY HEMOCHROMATOSIS AND DETERMINATION OF THE CRITICAL IRON LEVEL ASSOCIATED WITH FIBROSIS
    BASSETT, ML
    HALLIDAY, JW
    POWELL, LW
    [J]. HEPATOLOGY, 1986, 6 (01) : 24 - 29
  • [2] PRIMARY HEPATOCELLULAR-CARCINOMA IN IDIOPATHIC HEMOCHROMATOSIS AFTER REVERSAL OF CIRRHOSIS
    BLUMBERG, RS
    CHOPRA, S
    IBRAHIM, R
    CRAWFORD, J
    FARRAYE, FA
    ZELDIS, JB
    BERMAN, MD
    [J]. GASTROENTEROLOGY, 1988, 95 (05) : 1399 - 1402
  • [3] BRADBEAR RA, 1985, J NATL CANCER I, V75, P81
  • [4] BRADBEAR RA, 1987, NEOPLASMS LIVER, P191
  • [5] BRITTON RS, 1994, ADV EXP MED BIOL, V356, P239
  • [6] DETECTION OF BULKY DNA LESIONS IN THE LIVER OF PATIENTS WITH WILSONS-DISEASE AND PRIMARY HEMOCHROMATOSIS
    CARMICHAEL, PL
    HEWER, A
    OSBORNE, MR
    STRAIN, AJ
    PHILLIPS, DH
    [J]. MUTATION RESEARCH-FUNDAMENTAL AND MOLECULAR MECHANISMS OF MUTAGENESIS, 1995, 326 (02) : 235 - 243
  • [7] CHEVALLIER M, 1994, HEPATOLOGY, V20, P349, DOI 10.1002/hep.1840200213
  • [8] DEUGNIER Y, 1997, LIVER CANCER, P97
  • [9] PRENEOPLASTIC SIGNIFICANCE OF HEPATIC IRON-FREE FOCI IN GENETIC HEMOCHROMATOSIS - A STUDY OF 185 PATIENTS
    DEUGNIER, YM
    CHARALAMBOUS, P
    LEQUILLEUC, D
    TURLIN, B
    SEARLE, J
    BRISSOT, P
    POWELL, LW
    HALLIDAY, JW
    [J]. HEPATOLOGY, 1993, 18 (06) : 1363 - 1369
  • [10] PRIMARY LIVER-CANCER IN GENETIC HEMOCHROMATOSIS - A CLINICAL, PATHOLOGICAL, AND PATHOGENETIC STUDY OF 54 CASES
    DEUGNIER, YM
    GUYADER, D
    CRANTOCK, L
    LOPEZ, JM
    TURLIN, B
    YAOUANQ, J
    JOUANOLLE, H
    CAMPION, JP
    LAUNOIS, B
    HALLIDAY, JW
    POWELL, LW
    BRISSOT, P
    [J]. GASTROENTEROLOGY, 1993, 104 (01) : 228 - 234