Case of symptomatic propriospinal myoclonus evolving toward acute "myoclonic status"

被引:15
作者
Manconi, M [1 ]
Sferrazza, B [1 ]
Iannaccone, S [1 ]
Massimo, A [1 ]
Zucconi, M [1 ]
Ferini-Strambi, L [1 ]
机构
[1] Univ Vita Salute San Raffaele, IRCCS, Dept Neurol, I-20127 Milan, Italy
关键词
propriospinal myoclonus; sleep; myoclonic status; focal spinal myoclonus;
D O I
10.1002/mds.20645
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal-generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic "status" associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. (c) 2005 Movement Disorder Society.
引用
收藏
页码:1646 / 1650
页数:5
相关论文
共 14 条
  • [1] Atypical propriospinal myoclonus with possible relationship to α interferon therapy
    Benatru, I
    Thobois, S
    Andre-Obadia, N
    Gonnaud, PM
    Beaugendre, Y
    Berger, C
    Gonce, M
    Broussolle, E
    [J]. MOVEMENT DISORDERS, 2003, 18 (12) : 1564 - 1568
  • [2] BROWN P, 1991, BRAIN, V114, P197
  • [3] PROPRIOSPINAL MYOCLONUS - EVIDENCE FOR SPINAL PATTERN GENERATORS IN HUMANS
    BROWN, P
    ROTHWELL, JC
    THOMPSON, PD
    MARSDEN, CD
    [J]. MOVEMENT DISORDERS, 1994, 9 (05) : 571 - 576
  • [4] Chokroverty S, 1995, CLIN NEUROSCI, V3, P219
  • [5] PROPRIOSPINAL MYOCLONUS - A NEUROPHYSIOLOGIC ANALYSIS
    CHOKROVERTY, S
    WALTERS, A
    ZIMMERMAN, T
    PICONE, M
    [J]. NEUROLOGY, 1992, 42 (08) : 1591 - 1595
  • [6] Lyme neuroborreliosis presenting with propriospinal myoclonus
    delaSayette, V
    Schaeffer, S
    Queruel, C
    Bertran, F
    Defer, G
    Hazera, P
    Gallet, E
    [J]. JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1996, 61 (04) : 420 - 420
  • [7] Unique form of propriospinal myoclonus as a possible complication of an enteropathogenic toxin
    Espay, AJ
    Ashby, P
    Hanajima, R
    Jog, MS
    Lang, AE
    [J]. MOVEMENT DISORDERS, 2003, 18 (08) : 942 - 948
  • [8] PROPRIOSPINAL MYOCLONUS IN TETRAPLEGIC PATIENTS - CLINICAL, ELECTROPHYSIOLOGICAL AND THERAPEUTIC ASPECTS
    FOUILLET, N
    WIART, L
    ARNE, P
    ALAOUI, P
    PETIT, H
    BARAT, M
    [J]. PARAPLEGIA, 1995, 33 (11): : 678 - 681
  • [9] PROPRIOSPINAL MYOCLONUS IN MULTIPLE-SCLEROSIS
    KAPOOR, R
    BROWN, P
    THOMPSON, PD
    MILLER, DH
    [J]. JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1992, 55 (11) : 1086 - 1088
  • [10] Cannabis-induced propriospinal myoclonus
    Lozsadi, DA
    Forster, A
    Fletcher, NA
    [J]. MOVEMENT DISORDERS, 2004, 19 (06) : 708 - 709