Severe mitral stenosis as the first manifestation of systemic lupus erythematosus in a 20-year-old woman: the value of magnetic resonance imaging in the diagnosis of Libman-Sacks endocarditis
被引:7
作者:
Gouya, Herve
论文数: 0引用数: 0
h-index: 0
机构:
Hop Cochin, Serv Radiol A, F-75014 Paris, France
Paris Descartes Univ, Paris, FranceHop Cochin, Serv Radiol A, F-75014 Paris, France
Gouya, Herve
[1
,2
]
Cabanes, Laure
论文数: 0引用数: 0
h-index: 0
机构:
Paris Descartes Univ, Paris, FranceHop Cochin, Serv Radiol A, F-75014 Paris, France
Cabanes, Laure
[2
]
Mouthon, Luc
论文数: 0引用数: 0
h-index: 0
机构:
Paris Descartes Univ, Paris, France
INSERM, U1060, Paris, FranceHop Cochin, Serv Radiol A, F-75014 Paris, France
Mouthon, Luc
[2
,3
]
Pavie, Alain
论文数: 0引用数: 0
h-index: 0
机构:
Hop La Pitie Salpetriere, Paris, France
Univ Paris 06, Paris, FranceHop Cochin, Serv Radiol A, F-75014 Paris, France
Pavie, Alain
[4
,5
]
Legmann, Paul
论文数: 0引用数: 0
h-index: 0
机构:
Hop Cochin, Serv Radiol A, F-75014 Paris, France
Paris Descartes Univ, Paris, FranceHop Cochin, Serv Radiol A, F-75014 Paris, France
Legmann, Paul
[1
,2
]
Vignaux, Olivier
论文数: 0引用数: 0
h-index: 0
机构:
Hop Cochin, Serv Radiol A, F-75014 Paris, France
Paris Descartes Univ, Paris, FranceHop Cochin, Serv Radiol A, F-75014 Paris, France
Vignaux, Olivier
[1
,2
]
机构:
[1] Hop Cochin, Serv Radiol A, F-75014 Paris, France
Systemic lupus erythematosus;
Magnetic resonance imaging;
Libman-Sacks endocarditis;
Mitral stenosis;
D O I:
10.1007/s10554-014-0418-8
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
We report a case of severe mitral stenosis caused by Libman-Sacks endocarditis, as an initial manifestation of systemic lupus erythematosus (SLE) in a 20-year-old woman. Cardiac magnetic resonance imaging (MRI) demonstrated a thickening of the mitral valve with basal endocardial thickening exhibiting defect on first-pass perfusion short-axis acquisition and delayed enhancement in keeping with extensive fibrous endocarditis. The patient underwent successful mechanical mitral valve replacement. This case illustrates that MRI is useful in diagnosing this recognised but uncommon cardiac complication of SLE and excluding differential diagnosis such as valve tumour and infective endocarditis with perivalvular abscesses.