Hereditary angioedema

被引:565
作者
Zuraw, Bruce L. [1 ]
机构
[1] Vet Affairs Med Ctr, San Diego, CA 92161 USA
关键词
D O I
10.1056/NEJMcp0803977
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 19-year-old woman presents to the emergency department with light-headedness, severe abdominal pain, and intractable nausea and vomiting that began 12 hours earlier. The patient reports previous episodes of abdominal pain and swelling of her hands and feet that have been attributed possibly to food allergies, which have recently become more frequent. How should her case be evaluated and treated? Copyright © 2008 Massachusetts Medical Society.
引用
收藏
页码:1027 / 1036
页数:10
相关论文
共 54 条
[1]   HEREDITARY AND ACQUIRED C1-INHIBITOR DEFICIENCY - BIOLOGICAL AND CLINICAL CHARACTERISTICS IN 235 PATIENTS [J].
AGOSTONI, A ;
CICARDI, M .
MEDICINE, 1992, 71 (04) :206-215
[2]   Hereditary and acquired angioedema: Problems and progress: Proceedings of the third C1 esterase inhibitor deficiency workshop and beyond [J].
Agostoni, Angelo ;
Aygoeren-Puersuen, Emel ;
Binkley, Karen E. ;
Blanch, Alvaro ;
Bork, Konrad ;
Bouillet, Laurence ;
Bucher, Christoph ;
Castaldo, Anthony J. ;
Cicardi, Marco ;
Davis, Alvin E., III ;
De Carolis, Caterina ;
Drouet, Christian ;
Duponchel, Christiane ;
Farkas, Henriette ;
Fay, Kalman ;
Fekete, Bela ;
Fischer, Bettina ;
Fontana, Luigi ;
Fuest, George ;
Giacomelli, Roberto ;
Groener, Albrecht ;
Hack, C. Erik ;
Harmat, George ;
Jakenfelds, John ;
Juers, Mathias ;
Kalmar, Lajos ;
Kaposi, Pal N. ;
Karadi, Istvan ;
Kitzinger, Arianna ;
Kollar, Timea ;
Kreuz, Wolfhart ;
Lakatos, Peter ;
Longhurst, Hilary J. ;
Lopez-Trascasa, Margarita ;
Martinez-Saguer, Inmaculada ;
Monnier, Nicole ;
Nagy, Istvan ;
Nemeth, Eva ;
Nielsen, Erik Waage ;
Nuijens, Jan H. ;
O'Grady, Caroline ;
Pappalardo, Emanuela ;
Penna, Vincenzo ;
Perricone, Carlo ;
Perricone, Roberto ;
Rauch, Ursula ;
Roche, Olga ;
Rusicke, Eva ;
Spaeth, Peter J. ;
Szendei, George .
JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY, 2004, 114 (03) :S51-S131
[3]  
Binkley KE, 2000, J ALLERGY CLIN IMMUN, V106, P546
[4]  
Bissler JJ, 1997, P ASSOC AM PHYSICIAN, V109, P164
[5]   Hereditary angioedema: New findings concerning symptoms, affected organs, and course [J].
Bork, K ;
Meng, G ;
Staubach, P ;
Hardt, J .
AMERICAN JOURNAL OF MEDICINE, 2006, 119 (03) :267-274
[6]   Hereditary angioedema with normal C1-inhibitor activity in women [J].
Bork, K ;
Barnstedt, SE ;
Koch, P ;
Traupe, H .
LANCET, 2000, 356 (9225) :213-217
[7]   Treatment with C1 inhibitor concentrate in abdominal pain attacks of patients with hereditary angioedema [J].
Bork, K ;
Meng, G ;
Staubach, P ;
Hardt, J .
TRANSFUSION, 2005, 45 (11) :1774-1784
[8]   Hepatocellular adenomas in patients taking danazol for hereditary angio-oedema [J].
Bork, K ;
Pitton, M ;
Harten, P ;
Koch, P .
LANCET, 1999, 353 (9158) :1066-1067
[9]   Treatment of 193 episodes of laryngeal edema with C1 inhibitor concentrate in patients with hereditary angioedema [J].
Bork, K ;
Barnstedt, SE .
ARCHIVES OF INTERNAL MEDICINE, 2001, 161 (05) :714-718
[10]   Benefits and risks of danazol in hereditary angioedema: a long-term survey of 118 patients [J].
Bork, Konrad ;
Bygum, Anette ;
Hardt, Jochen .
ANNALS OF ALLERGY ASTHMA & IMMUNOLOGY, 2008, 100 (02) :153-161