Aquatherapy;
Ergometer training;
Motor function;
Quality of life;
Respiratory function;
Spinal muscular atrophy;
D O I:
10.12965/jer.1836604.302
中图分类号:
R49 [康复医学];
学科分类号:
100215 ;
摘要:
This study examined the effect of two different aerobic training modalities in a boy with spinal muscular atrophy type II. Motor functions were measured with Hammersmith Functional Motor Scale (HEMS) and Gross Motor Function Measure (GMFM). Spirometry was utilized for assessing pulmonary functions and PedsQL 3.0 Neuromuscular module was utilized for quality of life of child. Ergometer training was applied 3 times per week for the duration of 12 weeks. After 6 weeks of wash-out period, aquatherapy was applied for twice a week for the duration of 12 weeks. HEMS and GMFM scores, and pulmonary functions of the child and quality of life scores of his parents were improved during both mo- dates. These improvements were largely maintained during 1-year follow-up. This study showed that both modalities had similar effects on our case's pulmonary, motor functions and quality life of himself and parents. It will be a guide for researchers working in the area of children with neuromuscular disorders regarding plan and diversification of therapy program.
机构:
Boston Childrens Hosp, Dept Neurol, Boston, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Darras, B. T.
Connolly, A. M.
论文数: 0引用数: 0
h-index: 0
机构:
St Louis Childrens Hosp, Dept Neurol, St Louis, MO 63178 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Connolly, A. M.
Kuntz, N. L.
论文数: 0引用数: 0
h-index: 0
机构:
Ann & Robert H Lurie Childrens Hosp Chicago, Dept Pediat, Chicago, IL 60611 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Kuntz, N. L.
Kirschner, J.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Freiburg, Fac Med, Med Ctr, Dept Neuropediat & Muscle Disorders, Freiburg, GermanyNemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Kirschner, J.
Chiriboga, C. A.
论文数: 0引用数: 0
h-index: 0
机构:
Columbia Univ, Dept Neurol, New York, NY USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Chiriboga, C. A.
Saito, K.
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Womens Med Coll, Inst Med Genet, Tokyo, Japan
Tokyo Womens Med Coll, Dept Pediat, Tokyo, JapanNemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Saito, K.
Servais, L.
论文数: 0引用数: 0
h-index: 0
机构:
Inst Mot, Paris, FranceNemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
机构:
Columbia Univ, Dept Neurol, New York, NY USA
Columbia Univ, Dept Rehabil & Regenerat Med, New York, NY USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Montes, J.
Glanzman, A. M.
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Hosp Philadelphia, Dept Phys Therapy, Philadelphia, PA 19104 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Glanzman, A. M.
Bishop, K.
论文数: 0引用数: 0
h-index: 0
机构:
lonis Pharmaceut, Carlsbad, CA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Bishop, K.
Zhong, Z. J.
论文数: 0引用数: 0
h-index: 0
机构:
Biogen, Cambridge, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Zhong, Z. J.
Gheuens, S.
论文数: 0引用数: 0
h-index: 0
机构:
Biogen, Cambridge, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Gheuens, S.
Bennett, C. F.
论文数: 0引用数: 0
h-index: 0
机构:
lonis Pharmaceut, Carlsbad, CA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Bennett, C. F.
Schneider, E.
论文数: 0引用数: 0
h-index: 0
机构:
lonis Pharmaceut, Carlsbad, CA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Schneider, E.
Farwell, W.
论文数: 0引用数: 0
h-index: 0
机构:
Biogen, Cambridge, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Farwell, W.
De Vivo, D. C.
论文数: 0引用数: 0
h-index: 0
机构:
Columbia Univ, Dept Neurol, Med Ctr, New York, NY USA
Columbia Univ, Dept Pediat, Med Ctr, New York, NY 10027 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
机构:
Boston Childrens Hosp, Dept Neurol, Boston, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Darras, B. T.
Connolly, A. M.
论文数: 0引用数: 0
h-index: 0
机构:
St Louis Childrens Hosp, Dept Neurol, St Louis, MO 63178 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Connolly, A. M.
Kuntz, N. L.
论文数: 0引用数: 0
h-index: 0
机构:
Ann & Robert H Lurie Childrens Hosp Chicago, Dept Pediat, Chicago, IL 60611 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Kuntz, N. L.
Kirschner, J.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Freiburg, Fac Med, Med Ctr, Dept Neuropediat & Muscle Disorders, Freiburg, GermanyNemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Kirschner, J.
Chiriboga, C. A.
论文数: 0引用数: 0
h-index: 0
机构:
Columbia Univ, Dept Neurol, New York, NY USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Chiriboga, C. A.
Saito, K.
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Womens Med Coll, Inst Med Genet, Tokyo, Japan
Tokyo Womens Med Coll, Dept Pediat, Tokyo, JapanNemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Saito, K.
Servais, L.
论文数: 0引用数: 0
h-index: 0
机构:
Inst Mot, Paris, FranceNemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
机构:
Columbia Univ, Dept Neurol, New York, NY USA
Columbia Univ, Dept Rehabil & Regenerat Med, New York, NY USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Montes, J.
Glanzman, A. M.
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Hosp Philadelphia, Dept Phys Therapy, Philadelphia, PA 19104 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Glanzman, A. M.
Bishop, K.
论文数: 0引用数: 0
h-index: 0
机构:
lonis Pharmaceut, Carlsbad, CA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Bishop, K.
Zhong, Z. J.
论文数: 0引用数: 0
h-index: 0
机构:
Biogen, Cambridge, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Zhong, Z. J.
Gheuens, S.
论文数: 0引用数: 0
h-index: 0
机构:
Biogen, Cambridge, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Gheuens, S.
Bennett, C. F.
论文数: 0引用数: 0
h-index: 0
机构:
lonis Pharmaceut, Carlsbad, CA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Bennett, C. F.
Schneider, E.
论文数: 0引用数: 0
h-index: 0
机构:
lonis Pharmaceut, Carlsbad, CA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Schneider, E.
Farwell, W.
论文数: 0引用数: 0
h-index: 0
机构:
Biogen, Cambridge, MA USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA
Farwell, W.
De Vivo, D. C.
论文数: 0引用数: 0
h-index: 0
机构:
Columbia Univ, Dept Neurol, Med Ctr, New York, NY USA
Columbia Univ, Dept Pediat, Med Ctr, New York, NY 10027 USANemours Childrens Hosp, Dept Pediat, Div Neurol, 13535 Nemours Pkwy,5th Fl, Orlando, FL 32827 USA