Atypical Presentation of Cystic Fibrosis in An Infant

被引：0

作者：

Sahoo, Bandya ^{[1
,2
]}

Jain, Mukesh Kumar ^{[1
]}

Mishra, Reshmi ^{[1
]}

Patnaik, Sibabratta ^{[1
]}

机构：

[1] Kalinga Inst Med Sci, Dept Pediat, Bhubaneswar, Orissa, India

[2] Kalinga Inst Med Sci, Dept Pediat, Bhubaneswar 751015, Orissa, India

来源：

INDIAN JOURNAL OF DERMATOLOGY | 2022年 / 67卷 / 03期

关键词：

Cystic fibrosis; dermatitis; failure to thrive; ENTEROPATHICA-LIKE ERUPTION; DERMATITIS; DISEASE;

D O I：

10.4103/ijd.IJD_243_17

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Dermatitis as an initial manifestation of cystic fibrosis (CF) is unusual. The eruption is usually first noted in the perineum anywhere from several days to few months after birth. It subsequently spreads to the extremities and trunk. We report a 2-month-old male baby who presented with failure to thrive, hypoproteinemia, anemia, and a cutaneous eruption resembling acrodermatitis enteropathica. Oral zinc supplementation resulted in temporary resolution of the dermatitis. A further workup revealed the diagnosis of CF. The rash was responsive to nutritional and pancreatic enzyme supplementation.

引用

页码：287 / 289

页数：3

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