Meconium Ileus

被引:16
作者
Waldhausen, John H. T. [1 ]
Richards, Morgan [1 ]
机构
[1] Univ Washington, Seattle Childrens Hosp, Sch Med, Dept Surg, 4800 Sand Point Way NE, Seattle, WA 98105 USA
关键词
meconium ileus; cystic fibrosis; cystic fibrosis transmembrane conductance regulator; distal intestinal obstruction syndrome; epithelial sodium channels; fibrosing colonopathy; rectal prolapse; newborn intestinal obstruction; INTESTINAL-OBSTRUCTION SYNDROME; PANCREATIC-ENZYME SUPPLEMENTS; CYSTIC-FIBROSIS; GASTROINTESTINAL MANIFESTATIONS; RECTAL PROLAPSE; COLONOPATHY; CHILDREN; MANAGEMENT; SURVIVAL; OUTCOMES;
D O I
10.1055/s-0037-1609027
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Cystic fibrosis is one of the most common inheritable traits in Caucasians. Meconium ileus and its potential complications are the most likely reasons that these patients will need surgical care. Surgical intervention is usually needed in the neonatal period but may also be required later in life. This article discusses the various ways cystic fibrosis can affect the gastrointestinal tract. Both the operative and nonoperative management of complicated and uncomplicated meconium ileus are discussed in the neonatal period as well as long-term issues, such as distal intestinal obstructive syndrome, fibrosing colonopathy, and rectal prolapse, all of which may be seen in older children and adults.
引用
收藏
页码:121 / 126
页数:6
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