A Blue Baby Grows Up

被引：3
作者：
Aboulhosn, Jamil A. [1 ]
Child, John S. [1 ]
机构：
[1] Ahmanson UCLA Med Ctr Adult Congenital Heart Dis, Los Angeles, CA 90095 USA
来源：
CONGENITAL HEART DISEASE | 2009年 / 4卷 / 05期
关键词：
Cyanosis; Congenital Heart Disease; Adult; Single Ventricle; Pulmonary Hypertension; Tricuspid Atresia;
D O I：
10.1111/j.1747-0803.2009.00276.x
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
This report describes the history of a 41-year-old female patient born with atresia of the right atrioventricular valve, hypoplasia of the right ventricle, an atrial septal defect, and malposed great arteries. The patient underwent surgical pulmonary artery banding in infancy but did not undergo corrective surgery due to the development of pulmonary arterial hypertension. This report touches on several important clinical issues that may arise when caring for the adult with complex palliated cyanotic congenital heart disease, including the development and treatment of pulmonary arterial hypertension.
引用
收藏
页码：378 / 383
页数：6
相关论文
共 21 条
  • [1] Long-term oral bosentan treatment in patients with pulmonary arterial hypertension related to congenital heart disease: a 2-year study
    Apostolopoulou, S. C.
    Manginas, A.
    Cokkinos, D. V.
    Rammos, S.
    [J]. HEART, 2007, 93 (03) : 350 - 354
  • [2] Batista R J, 1997, Arq Bras Cardiol, V68, P279
  • [3] TRICUSPID ATRESIA - CLINICAL COURSE IN 101 PATIENTS
    DICK, M
    FYLER, DC
    NADAS, AS
    [J]. AMERICAN JOURNAL OF CARDIOLOGY, 1975, 36 (03) : 327 - 337
  • [4] Guidelines on diagnosis and treatment of pulmonary arterial hypertension -: The Task Force on Diagnosis and Treatment of Pulmonary Arterial Hypertension of the European Society of Cardiology
    Galiè, N
    Torbicki, A
    Barst, R
    Dartevelle, P
    Haworth, S
    Higenbottam, T
    Olschewski, H
    Peacock, A
    Pietra, G
    Rubin, LJ
    Simonneau, G
    [J]. EUROPEAN HEART JOURNAL, 2004, 25 (24) : 2243 - 2278
  • [5] Bosentan therapy in patients with Eisenmenger syndrome - A multicenter, double-blind, randomized, placebo-controlled study
    Galie, Nazzareno
    Beghetti, Maurice
    Gatzoulis, Michael A.
    Granton, John
    Berger, Rolf M. F.
    Lauer, Andrea
    Chiossi, Eleonora
    Landzberg, Michael
    [J]. CIRCULATION, 2006, 114 (01) : 48 - 54
  • [6] Atrial arrhythmia after surgical closure of atrial septal defects in adults
    Gatzoulis, MA
    Freeman, MA
    Siu, SC
    Webb, GD
    Harris, L
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1999, 340 (11) : 839 - 846
  • [7] Longer-term bosentan therapy improves functional capacity in Eisenmenger syndrome:: Results of the BREATHE-5 open-label extension study
    Gatzoulis, Michael A.
    Beghetti, Maurice
    Galie, Nazzareno
    Granton, John
    Berger, Rolf M. F.
    Lauer, Andrea
    Chiossi, Eleonora
    Landzberg, Michael
    [J]. INTERNATIONAL JOURNAL OF CARDIOLOGY, 2008, 127 (01) : 27 - 32
  • [8] Short- and long-term effects of inhaled iloprost therapy in children with pulmonary arterial hypertension
    Ivy, D. Dunbar
    Doran, Aimee K.
    Smith, Kelly J.
    Mallory, George B.
    Beghetti, Maurice
    Barst, Robyn J.
    Brady, Danicla
    Law, Yuk
    Parker, Donna
    Claussen, Lori
    Abman, Steven H.
    [J]. JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 2008, 51 (02) : 161 - 169
  • [9] Management of emergencies in adults with congenital cardiac disease
    Kaemmerer, Harald
    Bauer, Ulrike
    Pensl, Ulrike
    Oechslin, Erwin
    Gravenhorst, Verena
    Franke, Andreas
    Hager, Alfred
    Balling, Gunter
    Hauser, Michael
    Eicken, Andreas
    Hess, John
    [J]. AMERICAN JOURNAL OF CARDIOLOGY, 2008, 101 (04) : 521 - 525
  • [10] Pregnancy outcomes in women with congenital heart disease
    Khairy, P
    Ouyang, DW
    Fernandes, SM
    Lee-Parritz, A
    Economy, KE
    Landzberg, MJ
    [J]. CIRCULATION, 2006, 113 (04) : 517 - 524
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