A Blue Baby Grows Up

被引：3

作者：

Aboulhosn, Jamil A. ^{[1
]}

Child, John S. ^{[1
]}

机构：

[1] Ahmanson UCLA Med Ctr Adult Congenital Heart Dis, Los Angeles, CA 90095 USA

来源：

CONGENITAL HEART DISEASE | 2009年 / 4卷 / 05期

关键词：

Cyanosis; Congenital Heart Disease; Adult; Single Ventricle; Pulmonary Hypertension; Tricuspid Atresia;

D O I：

10.1111/j.1747-0803.2009.00276.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

This report describes the history of a 41-year-old female patient born with atresia of the right atrioventricular valve, hypoplasia of the right ventricle, an atrial septal defect, and malposed great arteries. The patient underwent surgical pulmonary artery banding in infancy but did not undergo corrective surgery due to the development of pulmonary arterial hypertension. This report touches on several important clinical issues that may arise when caring for the adult with complex palliated cyanotic congenital heart disease, including the development and treatment of pulmonary arterial hypertension.

引用

页码：378 / 383

页数：6

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