Giant Dermatofibrosarcoma Protuberans With Bilateral Orbital Involvement

被引:3
作者
Liou, Victor [1 ]
Chisholm, Smith Ann [1 ]
Logunova, Valentina [2 ]
Havlik, Robert [3 ]
Esmaili, Neda [1 ]
机构
[1] Med Coll Wisconsin, Dept Ophthalmol & Visual Sci, Milwaukee, WI 53226 USA
[2] Med Coll Wisconsin, Dept Pathol, Milwaukee, WI 53226 USA
[3] Med Coll Wisconsin, Dept Plast Surg, Milwaukee, WI 53226 USA
关键词
D O I
10.1097/IOP.0000000000001308
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
Dermatofibroma sarcoma protuberans (DFSP) is a rare, locally aggressive soft tissue sarcoma with a tendency for recurrence after excision. Although reports of unilateral orbital and bilateral eyelid disease exist, there have been no prior reports of DFSP with bilateral orbital involvement and no previously described cases of DFSP associated with transient optic neuropathy. The authors present a case report of a 34-year-old woman with a giant scalp DFSP involving the bilateral orbits. Despite radical resection with 5 cm margins where possible, multiple positive margins remained including deep positive margins at the bilateral superomedial retroseptal soft tissue. The patient completed adjuvant radiation for surgically unresectable disease. This case highlights the challenge of achieving local control given the disease extent and infiltration of the bilateral eyelids and orbits. This is the first reported case of DFSP with bilateral orbital involvement and associated transient optic neuropathy.
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页码:E36 / E39
页数:4
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