Primary splenic angiosarcoma in a 2.5-year-old boy with hepatic metastasis

被引:5
作者
Chen, Guangjie [1 ]
Li, Minju [1 ]
Wu, Dehua [1 ]
Tang, Hongfeng [1 ]
Tang, Daxing [1 ]
机构
[1] Zhejiang Univ, Sch Med, Childrens Hosp, Hangzhou 310003, Zhejiang, Peoples R China
关键词
Angiosarcoma; Spleen; Child; Chemotherapy; Surgery; SPLEEN; CHILD;
D O I
10.1007/s00383-012-3164-9
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Primary splenic angiosarcoma in children is extremely rare and has a very poor prognosis. We reported a 2.5-year-old boy who had this rare entity and hepatic metastasis. The patient presented with left upper quadrant abdominal mass and anemia. The patient received multidisciplinary treatment and died 32 months after splenectomy.
引用
收藏
页码:1147 / 1150
页数:4
相关论文
共 21 条
[1]  
ALT B, 1985, Pediatric Pathology, V4, P331
[2]  
CHABALKO J J, 1975, Medical and Pediatric Oncology, V1, P135, DOI 10.1002/mpo.2950010208
[3]  
CHEN KTK, 1979, ARCH PATHOL LAB MED, V103, P122
[4]  
Delacruz V, 2005, ARCH PATHOL LAB MED, V129, P1054
[5]   Metastasized angiosarcoma of the spleen in a 2-year-old girl [J].
den Hoed, IDM ;
Granzen, B ;
Aronson, DC ;
Pauwels, P ;
de Kraker, J ;
van Heurn, LWE .
PEDIATRIC HEMATOLOGY AND ONCOLOGY, 2005, 22 (05) :387-390
[6]   PRIMARY ANGIOSARCOMA OF THE SPLEEN - A CLINICOPATHOLOGICAL STUDY OF 40 CASES [J].
FALK, S ;
KRISHNAN, J ;
MEIS, JM .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1993, 17 (10) :959-970
[7]  
FERRARA A, 1955, Rass Fisiopatol Clin Ter, V27, P759
[8]  
Garlock JH, 1940, J MT SANAI HOSP, V6, P391
[9]  
HA HK, 1994, ACTA RADIOL, V35, P455
[10]   Primary angiosarcoma of the spleen [J].
Hsu, JT ;
Chen, HM ;
Lin, CY ;
Yeh, CN ;
Hwang, TL ;
Jan, YY ;
Chen, MF .
JOURNAL OF SURGICAL ONCOLOGY, 2005, 92 (04) :312-316