A child with pulmonary and liver Langerhans'-cell histiocytosis

被引：3

作者：

Ma Xiao-li ^{[1
]}

Shen Kun-ling ^{[1
]}

Wang Bin ^{[1
]}

机构：

[1] Capital Med Univ, Beijing Childrens Hosp Affiliated, Hematol Ctr, Beijing 100045, Peoples R China

来源：

CHINESE MEDICAL JOURNAL | 2012年 / 125卷 / 09期

关键词：

Langerhans'-cell histiocytosis; pulmonary; liver; child;

D O I：

10.3760/cma.j.issn.0366-6999.2012.09.031

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Clinical categories of Langerhans cell histiocytosis (LCH) include single and multi-system disease. Pulmonary LCH is rare, which is an unusual interstitial lung disease with the characteristics of monoclonal proliferation and infiltration of Langerhans cells to organs. We report our experience of a rare LCH case of multiple organs such as pulmonary and liver as the main clinical manifestation. The patient was treated with chemotherapy which included prednisone, vinblastine, methotrexate and 6-mercaptopurine for 52 weeks and follow up all along. The patient has a favorable clinical outcome. Chin Med J 2012;125(9):1675-1676

引用

页码：1675 / 1676

页数：2

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