Diffuse central nervous system lupus involving white matter, basal ganglia, thalami and brainstem

被引:23
作者
Shibata, M
Kibe, T
Fujimoto, S
Ishikawa, T
Murakami, M
Ichiki, T
Wada, Y
机构
[1] Nagoya City Univ, Sch Med, Dept Pediat, Mizuho Ku, Nagoya, Aichi 4678601, Japan
[2] Nagoya City Univ, Sch Med, Dept Lab Med, Mizuho Ku, Nagoya, Aichi 4678601, Japan
[3] Kainan Hosp, Dept Pediat, Yatomi, Aichi, Japan
关键词
systemic lupus erythematosus; magnetic resonance imaging; basal ganglia; acute encephalopathy; central nervous system lupus;
D O I
10.1016/S0387-7604(99)00027-3
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We described an 11-year-old girl with acute central nervous system lupus showing diffuse lesions. She developed generalized convulsions followed by prolonged coma, and her psychomotor ability recovered fully after 3 months of steroid therapy. Cranial magnetic resonance imaging (MRI) showed high signal intensity in the cerebral deep white matter, bilateral basal ganglia, thalami, and brainstem on T2-weighted image. These lesions resolved over 1 month with residual atrophic change in the heads of the caudate nucleus on MRI. Acute SLE leukoencephalopathy may be recognized as a subtype of CNS lupus. (C) 1999 Elsevier Science B.V. All rights reserved.
引用
收藏
页码:337 / 340
页数:4
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