Surgical repair of congenital coronary artery fistula: A case report

Coronary artery fistula is an exceedingly uncommon congenital disorder characterized by fistulous communication of a coronary artery with asystemic or pulmonary vessel or a heart chamber. Small fistulas are asymptomatic and benign while large fistulas present in a variety of ways like heart failure, arrhythmias or endocarditis. We report here a rare case of eight years old girl who presented to us with history of shortness of breath and palpitation. Her echocardiography revealed a moderately large right coronary artery fistula that was opening into right ventricle. Angiography later confirmed its presence. We surgically closed it with a pericardial patch on cardiopulmonary bypass. The girl showed uneventful recovery and her postoperative echocardiography revealed no residual fistula. She was discharged on 5th postoperative day and her follow up was also unremarkable.