Pulmonary hypertension in POEMS syndrome: resolution following radiotherapy

被引：2

作者：

Brewis, Melanie J. ^{[1
]}

Church, Alistair C. ^{[1
]}

Peacock, Andrew J. ^{[1
]}

Thomson, Stephen ^{[1
]}

Tighe, Jane ^{[2
]}

Johnson, Martin K. ^{[1
]}

机构：

[1] Golden Jubilee Natl Hosp, Scottish Pulm Vasc Unit, Level 1,Agamemnon St, Glasgow G81 4DY, Lanark, Scotland

[2] Aberdeen Royal Infirm, Dept Haematol, Aberdeen, Scotland

来源：

PULMONARY CIRCULATION | 2014年 / 4卷 / 04期

关键词：

plasmacytoma; sildenafil; bosentan;

D O I：

10.1086/678553

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Pulmonary hypertension (PH) is defined by the presence of a mean pulmonary artery pressure (mPAP) >= 25 mmHg. It may be idiopathic or arise as a consequence of a number of diverse conditions. PH has been reported in association with POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal plasma cell disorder, and skin changes), with reversal following systemic treatment with corticosteroids. We report a case of pulmonary hypertension associated with POEMS syndrome treated with radical radiotherapy locally to bone lesions with resolution of systemic disease.

引用

页码：732 / 735

页数：4

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