The diagnosis of von Willebrand disease: A guideline from the UK Haemophilia Centre Doctors' Organization

被引：115

作者：

Laffan, M

Brown, SA

Collins, PW

Cumming, AM

Hill, FGH

Keeling, D

Peake, IR

Pasi, KJ

机构：

[1] Barts & London, Queen Marys Sch Med & Dent, Dept Haematol, UKHCDO von Willebrands Dis Working Party, London E1 2AD, England

[2] Hammersmith Hosp, Imperial Coll, Dept Haematol, London, England

[3] Royal Free Hosp, Dept Haematol, London NW3 2QG, England

[4] Univ Wales Hosp, Dept Haematol, Cardiff CF4 4XN, S Glam, Wales

[5] Manchester Royal Infirm, Dept Haematol, Manchester M13 9WL, Lancs, England

[6] Birmingham Childrens Hosp, Dept Haematol, Birmingham, W Midlands, England

[7] Churchill Hosp, Dept Haematol, Oxford OX3 7LJ, England

[8] Royal Hallamshire Hosp, Div Genom Med, Sheffield S10 2JF, S Yorkshire, England

来源：

HAEMOPHILIA | 2004年 / 10卷 / 03期

关键词：

bleeding; diagnosis; guidelines; haemostasis; UKHCDO; von Willebrand;

D O I：

10.1111/j.1365-2516.2004.00894.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

von Willebrand disease (VWD) is the commonest inherited bleeding disorder. However, despite an increasing understanding of the pathophysiology of VWD, the diagnosis of VWD is frequently difficult because of uncertainty regarding the relationship between laboratory assays and function in vivo. The objective of this guideline is to provide contemporary advice on a rational approach to the diagnosis of VWD. This is the second edition of this UK Haemophilia Centre Doctors' Organisation (UKHCDO) guideline and supersedes the previous edition which was published in 1997.

引用

页码：199 / 217

页数：19

共 90 条

[1]

ABILDGAARD CF, 1980, BLOOD, V56, P712

[2] DEVELOPMENT OF THE HUMAN COAGULATION SYSTEM IN THE FULL-TERM INFANT [J].

ANDREW, M ;

PAES, B ;

MILNER, R ;

JOHNSTON, M ;

MITCHELL, L ;

TOLLEFSEN, DM ;

POWERS, P .

BLOOD, 1987, 70 (01) :165-172

[3] INCREASES IN FACTOR-VIII COMPLEX AND FIBRINOLYTIC-ACTIVITY ARE DEPENDENT ON EXERCISE INTENSITY [J].

ANDREW, M ;

CARTER, C ;

OBRODOVICH, H ;

HEIGENHAUSER, G .

JOURNAL OF APPLIED PHYSIOLOGY, 1986, 60 (06) :1917-1922

[4]

BENNETT B, 1972, J LAB CLIN MED, V80, P256

[5]

BURGESS C, 2001, HAEMOPHILIA, pB247

[6] Significant linkage and non-linkage of type 1 von Willebrand disease to the von Willebrand factor gene [J].

Casaña, P ;

Martínez, F ;

Haya, S ;

Espinós, C ;

Aznar, JA .

BRITISH JOURNAL OF HAEMATOLOGY, 2001, 115 (03) :692-700

[7] DEMONSTRATION THAT VENOUS OCCLUSION FAILS TO RELEASE VON-WILLEBRAND-FACTOR MULTIMERS [J].

CASONATO, A ;

PONTARA, E ;

BERTOMORO, A ;

DANNHAUSER, D ;

SARTORI, MT ;

PATRASSI, G ;

BOERI, G ;

GIROLAMI, A .

BLOOD COAGULATION & FIBRINOLYSIS, 1995, 6 (06) :574-578

[8] Von Willebrand factor collagen binding activity in the diagnosis of von Willebrand disease: an alternative to ristocetin co-factor activity? [J].

Casonato, A ;

Pontara, E ;

Bertomoro, A ;

Sartorello, F ;

Cattini, MG ;

Girolami, A .

BRITISH JOURNAL OF HAEMATOLOGY, 2001, 112 (03) :578-583

[9]

Castaman G, 1999, THROMB HAEMOSTASIS, V82, P1065

[10] PATIENTS WITH SEVERE VON-WILLEBRAND DISEASE ARE INSENSITIVE TO THE RELEASING EFFECT OF DDAVP - EVIDENCE THAT THE DDAVP-INDUCED INCREASE IN PLASMA FACTOR-VIII IS NOT SECONDARY TO THE INCREASE IN PLASMA VON-WILLEBRAND-FACTOR [J].

CATTANEO, M ;

SIMONI, L ;

GRINGERI, A ;

MANNUCCI, PM .

BRITISH JOURNAL OF HAEMATOLOGY, 1994, 86 (02) :333-337

← 1 2 3 4 5 6 7 8 9 →