Valve-sparing replacement of the ascending aorta and aortic arch in a child with Loeys-Dietz syndrome

被引：7

作者：

Ozker, Emre ^{[1
]}

Vuran, Can ^{[1
]}

Saritas, Bulent ^{[1
]}

Turkoz, Riza ^{[1
]}

机构：

[1] Baskent Univ, Istanbul Med & Res Hosp, Dept Cardiovasc Surg, Istanbul, Turkey

来源：

EUROPEAN JOURNAL OF CARDIO-THORACIC SURGERY | 2012年 / 41卷 / 05期

关键词：

Aortic aneurysm; Aortic arch replacement; Valve-sparing surgery; MUTATIONS; ANEURYSM;

D O I：

10.1093/ejcts/ezr235

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We describe a successful surgical treatment in a 2.5-year old boy with Loeys-Dietz syndrome, in whom we performed aortic arch and ascending aorta replacement with a valve-sparing operation (VSO) of the aortic root because of significant aortic insufficiency and dilation of the aortic root. We believe that VSO is ideal for treating young patients with aortic root aneurysm with normal or minimally diseased aortic cusps to avoid the disadvantages of prosthetic valve replacements.

引用

页码：1184 / 1185

页数：2

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