Orthotopic liver transplantation for polycystic liver disease with massive hepatomegaly

被引：0

作者：

Dreger, N. M. ^{[1
]}

Kaiser, G. M. ^{[1
]}

Treckmann, J. W. ^{[1
]}

Mathe, Z. ^{[1
]}

Benkoe, T. ^{[1
]}

Paul, A. ^{[1
]}

机构：

[1] Univ Klinikum Essen, Klin Allgemeinchirurg Viszeral & Transplantat Chi, D-45147 Essen, Germany

来源：

DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT | 2013年 / 138卷 / 47期

关键词：

polycystic liver disease; orthotopic liver transplantation; hepatomegaly; RANDOMIZED CONTROLLED-TRIAL; LONG-ACTING OCTREOTIDE; EVEROLIMUS; VOLUME; MODEL;

D O I：

10.1055/s-0033-1349654

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

History: A 51-year-old man (126kg, 192cm) with massive hepatomegaly causing cardiopulmonary symptoms was referred to our transplant center 14 years after initial diagnosis of polycystic liver disease. Treatment and course: Uneventful hepatectomy was followed by orthotopic liver transplantation using caval replacement. Donor liver came from a 73-year-old woman (extended criteria donor organ offer). A portocaval shunting was not established during transplantation although the explanted liver weighed 22kg. 18 months after transplantation liver function is stable and the patient enjoys normal quality of life. Conclusion: This case report demonstrates the value and success of transplantation for patients suffering from enormous hepatomegaly due to polycystic liver disease.

引用

页码：2407 / 2409

页数：3

共 14 条

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