Pregnancy with aortic dissection in Ehler-Danlos syndrome. Staged replacement of the total aorta (10-year follow-up)

被引:14
作者
Babatasi, G
Massetti, M
Bhoyroo, S
Khayat, A
机构
[1] Dept. Thorac. and Cardiovasc. Surg., Univ. Hosp. CHU Caen, 14033 Caen, Cote de Nacre
关键词
Ehlers-Danlos syndrome; Marfan syndrome; aortic dissection; pregnancy;
D O I
10.1016/S1010-7940(97)00211-X
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Pregnancy complicated by aortic dissection in patients with hereditary disorder of connective tissue presents interesting considerations including management of caesarean section with the unexpected need for cardiac surgery in emergency. Generalizations can be made on managment principles with long-term follow-up requiring an aggressive individualized approach by a multidisciplinary team. A 33-year-old parturient presenting an aortic dissection at 37 weeks gestation required prompt diagnosis of Ehlers-Danlos syndrome in combination with correct surgical therapy resulted in the survival of both the mother and infant. During the 10-year follow-up, multiple complex dissection required transverse aortic arch and thoracoabdominal aortic replacement. (C) 1997 Elsevier Science B.V.
引用
收藏
页码:671 / 674
页数:4
相关论文
共 11 条
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