Safety and efficacy of pirfenidone in patients carrying telomerase complex mutation

被引:27
作者
Justet, Aurelien [1 ,2 ]
Thabut, Gabriel [2 ,3 ]
Manali, Effrosyni [4 ]
Molina Molina, Maria [5 ]
Kannengiesser, Caroline [6 ]
Cadranel, Jacques [7 ]
Cottin, Vincent [8 ]
Gondouin, Anne [9 ]
Nunes, Hilario [10 ]
Magois, Eline [11 ]
Tromeur, Cecile [12 ]
Prevot, Gregoire [13 ]
Papiris, Spyros [4 ]
Marchand-Adam, Sylvain [14 ]
Gamez, Anne Sophie [15 ]
Reynaud-Gaubert, Martine [16 ]
Wemeau, Lidwine [17 ]
Crestani, Bruno [1 ,2 ]
Borie, Raphael [1 ,2 ]
机构
[1] Hop Bichat Claude Bernard, AP HP, Serv Pneumol A, DHU FIRE, Paris, France
[2] Univ Paris Diderot, INSERM, Unite 1152, Paris, France
[3] Hop Bichat Claude Bernard, AP HP, Serv Pneumol B, Paris, France
[4] Univ Athens, Athens Med Sch, Attikon Univ Hosp, Resp Med Dept, Athens, Greece
[5] Univ Hosp Bellvitge, Dept Pneumol, Unit Interstitial Lung Dis, Barcelona, Spain
[6] Univ Paris Diderot, Hop Bichat, AP HP, Dept Genet, Paris, France
[7] Hop Tenon, AP HP, Serv Pneumol, Malad Pulmonaires Rares, Paris, France
[8] Univ Claude Bernard Lyon 1, Hop Louis Pradel, Serv Pneumol, Lyon, France
[9] CHU Besancon, Serv Pneumol, Besancon, France
[10] Hop Avicenne, AP HP, Serv Pneumol, Malad Pulmonaires Rares, Bobigny, France
[11] Univ Picardie Jules Verne, Hop Amiens, Serv Pneumol, Amiens, France
[12] Univ Europeenne Bretagne, Dept Mede Interne & Pneumol, CHU Cavale Blanche, UBO,GETBO EA3878,IFR 148, Brest, France
[13] Hop Larrey, Serv Pneumol, Toulouse, France
[14] CHU Tours, Serv Pneumol & Explorat Fonct Resp, Tours, France
[15] CHU Montpellier, Hop Arnaud de Villeneuve, Dept Pneumol & Addictol, Montpellier, France
[16] Hop Nord Marseille, Serv Pneumol, Marseille, France
[17] CHRU Lille, Serv Pneumol, Lille, France
关键词
IDIOPATHIC PULMONARY-FIBROSIS;
D O I
10.1183/13993003.01875-2017
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页数:4
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