Safety and efficacy of pirfenidone in patients carrying telomerase complex mutation

被引：27

作者：

Justet, Aurelien ^{[1
,2
]}

Thabut, Gabriel ^{[2
,3
]}

Manali, Effrosyni ^{[4
]}

Molina Molina, Maria ^{[5
]}

Kannengiesser, Caroline ^{[6
]}

Cadranel, Jacques ^{[7
]}

Cottin, Vincent ^{[8
]}

Gondouin, Anne ^{[9
]}

Nunes, Hilario ^{[10
]}

Magois, Eline ^{[11
]}

Tromeur, Cecile ^{[12
]}

Prevot, Gregoire ^{[13
]}

Papiris, Spyros ^{[4
]}

Marchand-Adam, Sylvain ^{[14
]}

Gamez, Anne Sophie ^{[15
]}

Reynaud-Gaubert, Martine ^{[16
]}

Wemeau, Lidwine ^{[17
]}

Crestani, Bruno ^{[1
,2
]}

Borie, Raphael ^{[1
,2
]}

机构：

[1] Hop Bichat Claude Bernard, AP HP, Serv Pneumol A, DHU FIRE, Paris, France

[2] Univ Paris Diderot, INSERM, Unite 1152, Paris, France

[3] Hop Bichat Claude Bernard, AP HP, Serv Pneumol B, Paris, France

[4] Univ Athens, Athens Med Sch, Attikon Univ Hosp, Resp Med Dept, Athens, Greece

[5] Univ Hosp Bellvitge, Dept Pneumol, Unit Interstitial Lung Dis, Barcelona, Spain

[6] Univ Paris Diderot, Hop Bichat, AP HP, Dept Genet, Paris, France

[7] Hop Tenon, AP HP, Serv Pneumol, Malad Pulmonaires Rares, Paris, France

[8] Univ Claude Bernard Lyon 1, Hop Louis Pradel, Serv Pneumol, Lyon, France

[9] CHU Besancon, Serv Pneumol, Besancon, France

[10] Hop Avicenne, AP HP, Serv Pneumol, Malad Pulmonaires Rares, Bobigny, France

[11] Univ Picardie Jules Verne, Hop Amiens, Serv Pneumol, Amiens, France

[12] Univ Europeenne Bretagne, Dept Mede Interne & Pneumol, CHU Cavale Blanche, UBO,GETBO EA3878,IFR 148, Brest, France

[13] Hop Larrey, Serv Pneumol, Toulouse, France

[14] CHU Tours, Serv Pneumol & Explorat Fonct Resp, Tours, France

[15] CHU Montpellier, Hop Arnaud de Villeneuve, Dept Pneumol & Addictol, Montpellier, France

[16] Hop Nord Marseille, Serv Pneumol, Marseille, France

[17] CHRU Lille, Serv Pneumol, Lille, France

来源：

EUROPEAN RESPIRATORY JOURNAL | 2018年 / 51卷 / 03期

关键词：

IDIOPATHIC PULMONARY-FIBROSIS;

D O I：

10.1183/13993003.01875-2017

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

引用

页数：4

共 12 条

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